{"id":19,"date":"2023-02-13T13:51:56","date_gmt":"2023-02-13T13:51:56","guid":{"rendered":"https:\/\/new.vwdtest.com\/se\/?page_id=19"},"modified":"2024-04-03T07:08:59","modified_gmt":"2024-04-03T07:08:59","slug":"von-willebrand-disease","status":"publish","type":"page","link":"https:\/\/vwdtest.com\/rs\/von-willebrand-disease\/","title":{"rendered":"Saznajte vi\u0161e o von Willebrandovoj bolesti"},"content":{"rendered":"<div class=\"default-block container\">\n<h2><strong>Von Willebrandova bolest (VWD) <\/strong><br><strong>je naj\u010de\u0161\u0107i poreme\u0107aj krvarenja<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<h5 class=\"bleeding-symptoms-title live\">Kada je krvni sud povre\u0111en, deo crvenih krvnih zrnaca se slepljuje kako bi zatvorili ranu i zaustavili krvarenje. Taj se proces naziva zgru\u0161avanje. Kod osoba s poreme\u0107ajima krvarenja, kao \u0161to su VWD ili hemofilija, zgru\u0161avanje krvi ne funkcioni\u0161e pravilno. Zato su <strong>osobe s VWD-om sklonije \u010de\u0161\u0107em i dugotrajnijem krvarenju<\/strong>, na primer <a href=\"https:\/\/vwdtest.com\/rs\/bleeding-symptoms\/#nosebleed\">krvarenju iz nosa<\/a>, <a href=\"https:\/\/vwdtest.com\/rs\/bleeding-symptoms\/#oral-bleed\">krvarenju desni<\/a> ili nakon<a href=\"https:\/\/vwdtest.com\/rs\/bleeding-symptoms\/#minor-wounds\"> manje povrede<\/a>. \u017dene s VWD-om \u010desto imaju <a href=\"https:\/\/vwdtest.com\/rs\/bleeding-symptoms\/#hmb\">obilno menstrualno krvarenje<\/a>. Kod osoba s VWD-om krvarenje je uzrokovano nedostatkom proteina von Willebrandovog faktora (VWF), koji je va\u017ean za zgru\u0161avanje krvi.<sup>1<\/sup><\/h5>\n<\/div>\n\n<img decoding=\"async\" src=\"https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/02\/hero2.webp\" alt=\"Saznajte vi\u0161e o von Willebrandovoj bolesti\" class=\"page_thumbnail d-xl-none\">\r\n\n\n<div class=\"default-block container\">\n<figure class=\"wp-block-image size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"1024\" height=\"510\" src=\"https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/03\/Illustration-01-1024x510-1.png\" alt=\"\" class=\"wp-image-323\" srcset=\"https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/03\/Illustration-01-1024x510-1.png 1024w, https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/03\/Illustration-01-1024x510-1-300x149.png 300w, https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/03\/Illustration-01-1024x510-1-768x383.png 768w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>Von Willebrandov faktor (VWF) va\u017ean je za zgru\u0161avanje krvi<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VWF je protein koji cirkuli\u0161e u krvi. Proizvode ga \u0107elije u krvnim sudovima i kostima i otpu\u0161taju ga u krvotok. U slu\u010daju povrede, <strong>VWF zajedno s drugim proteinima dovodi do zaustavljanju krvarenja stvaranjem krvnog ugru\u0161ka<\/strong>. Kod osoba s VWD-om telo ne proizvodi dovoljno VWF-a ili protein ne funkcioni\u0161e normalno. Usled toga ni zgru\u0161avanje krvi ne funkcioni\u0161e normalno i krvarenje mo\u017ee biti dugotrajnije.<sup>2<\/sup><\/p>\n<\/div>\n\n\r\n\r\n<div class=\"styledBox\">\r\n    <h2 class=\"styledBox__title\">Postoje tri glavna tipa VWD-a<\/h2>\r\n\r\n    <ul class=\"styledBox__list\">\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD tip 1: <\/strong>Otprilike 3 od 4 osobe s VWD-om pate od tipa 1, \u0161to ga \u010dini naj\u010de\u0161\u0107im tipom bolesti. Te osobe imaju nizak nivo proteina VWF.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD tip 2:<\/strong> Kod osoba s VWD-om tipa 2 VWF protein ne funkcioni\u0161e pravilno.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD tip 3:<\/strong> \u010cesto je te\u017ei od tipa 1 ili 2, a radi se o najre\u0111em obliku ove bolesti. Osobe s VWD-om tipa 3 imaju vrlo nizak nivo proteina VWF.<sup>2<\/sup><\/p>\n        <\/li>\r\n        <\/ul>\r\n<\/div>\n\n<div class=\"default-block container\">\n<h2>Koja je razlika izme\u0111u VWD-a i hemofilije?<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">I VWD i hemofilija su poreme\u0107aji krvarenja. Osobe koje pate od obe bolesti imaju pove\u0107an rizik od krvarenja, me\u0111utim kod osoba s VWD-om i osoba s hemofilijom do krvarenja obi\u010dno ne dolazi na istim delovima tela. Ovi poreme\u0107aji su uzrokovani nedostatkom razli\u010ditih proteina: VWD je uzrokovan nedostatkom proteina VWF, dok hemofilija nastaje zbog delimi\u010dnog ili potpunog nedostatka  faktora VIII i  IX. Ovi razli\u010diti uzroci ukazuju i na razli\u010dite na\u010dine le\u010denja ovih bolesti.<sup>3,4<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>VWD se mo\u017ee le\u010diti<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Ne postoji lek za VWD, ali postoje <a href=\"https:\/\/vwdtest.com\/rs\/i-live-with-vwd\/\">delotvorne terapije<\/a>. Osobe s VWD-om ve\u0107inom imaju vrlo blage simptome s kojima se mogu sami nositi u svakodnevnom \u017eivotu. Me\u0111utim, osobe s te\u0161kim oblicima VWD-a mogu imati ozbiljnija i \u010de\u0161\u0107a krvarenja, s ve\u0107im uticajem na \u017eivot.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>Ako imate VWD, va\u017eno je da se javite lokalnom centru za le\u010denje koji je specijalizovan za poreme\u0107aje krvarenja.<\/strong> Osoblje u <a href=\"https:\/\/vwdtest.com\/rs\/helpful-resources\/\">centru za le\u010denje<\/a> odgovori\u0107e na sva va\u0161a pitanja i voditi vas u zbrinjavanju bolesti kako biste mogli \u017eiveti normalnim \u017eivotom.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Uz to vam savetujemo da stupite u kontakt s lokalnim<a href=\"https:\/\/vwdtest.com\/rs\/helpful-resources\/\"> udru\u017eenjima pacijenata<\/a>. Ima vi\u0161e ljudi s poreme\u0107ajima krvarenja nego \u0161to mislite i rado \u0107e podeliti svoja iskustva sa vama.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-3 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"259\" height=\"325\" src=\"https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/02\/Illustration-03.png\" alt=\"\" class=\"wp-image-26\" srcset=\"https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/02\/Illustration-03.png 259w, https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/02\/Illustration-03-239x300.png 239w\" sizes=\"(max-width: 259px) 100vw, 259px\" \/><\/figure>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<h2>Mogu\u0107e je da od VWD-a pati do 1% svetske populacije<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>VWD je nasledna bolest koja poga\u0111a i mu\u0161karce i \u017eene razli\u010dite starosti, uklju\u010duju\u0107i i decu. Kod \u017eena je verovatno\u0107a nastanka simptoma VWD-a ve\u0107a nego kod mu\u0161karaca zbog krvarenja koje se javlja tokom  menstruacije, trudno\u0107e i poro\u0111aja.<br><br><strong>Mnogi ljudi imaju blage simptome i mo\u017eda i ne znaju da imaju VWD.<\/strong><br><br><\/p>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-8 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-6 wp-block-columns\">\n<div class=\"is-layout-flow wp-block-column\"><div class=\"default-block container\">\n<h2><strong>\u010cesto osobe s VWD-om <strong>godinama<\/strong><\/strong> <strong>\u010dekaju na dijagnozu<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>\u010cesto je te\u0161ko utvrditi da li je krvarenje normalno. \u0160tavi\u0161e, mnogi ljudi nisu ni svesni poreme\u0107aja krvarenja kao \u0161to je VWD. Zato osobe s VWD-om \u010desto moraju da \u010dekaju i nekoliko godina od pojave prvih simptoma krvarenja do kona\u010dne dijagnoze. Pritom pacijentkinje \u010dekaju du\u017ee od pacijenata. <strong>Bez dijagnoze i le\u010denja pacijenti mogu patiti od \u010destih krvarenja, nedostatka gvo\u017e\u0111a, bolova i smanjenog kvaliteta \u017eivota. <\/strong>\u010cak i ako su simptomi krvarenja u svakodnevnom \u017eivotu blagi, postoji rizik od ozbiljnog krvarenja tokom operacije ili nakon povrede.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p>Zato<strong> je va\u017eno je biti svestan simptoma krvarenja i poreme\u0107aja krvarenja kao \u0161to je VWD.<\/strong> Ako ste u nedoumici u vezi bilo kojeg krvarenja, uradite na\u0161 test krvarenja.<\/p>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full is-style-default\"><img decoding=\"async\" loading=\"lazy\" width=\"480\" height=\"331\" src=\"https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/02\/Fill-47-1.png\" alt=\"\" class=\"wp-image-50\" srcset=\"https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/02\/Fill-47-1.png 480w, https:\/\/vwdtest.com\/rs\/wp-content\/uploads\/sites\/57\/2023\/02\/Fill-47-1-300x207.png 300w\" sizes=\"(max-width: 480px) 100vw, 480px\" \/><\/figure>\n<\/div><\/div>\n<\/div>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>Za dijagnostikovanje VWD-a potrebni su istorija krvarenja i laboratorijske<\/strong> <strong>analize<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VWD je retka bolest i nije svaki lekar upoznat s njom. Zato bi <strong>kona\u010dnu dijagnozu trebalo da postavi lekar specijalista za poreme\u0107aje krvarenja<\/strong>. Dijagnoza VWD-a obavezno obuhvata celi proces. Va\u0161 lekar treba za po\u010detak da bude upoznat sa bilo kakvom istorijom krvarenja kod vas i \u010dlanova va\u0161e porodice. Kako bi ocenio celokupnu istoriju krvarenja, lekar \u0107e vam postaviti niz pitanja. Ako istorija krvarenja ukazuje na to da mo\u017eda imate poreme\u0107aj krvarenja, krv vam mora biti analizirana u specijalizovanoj laboratoriji.<sup>1<\/sup> Na osnovu rezultata krvnih analiza lekar \u0107e postaviti kona\u010dnu dijagnozu.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>\u0160to pre dobijete dijagnozu, pre \u0107ete mo\u0107i da po\u010dnete da donosite informisane odluke o svom le\u010denju i na\u010dinu \u017eivota.<\/strong><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h6>Literatura<\/h6>\n<\/div>\n\n<div class=\"default-block container\">\n<ol><div class=\"default-block container\">\n<li>Corrales-Medina FF et al. <em>Blood Rev <\/em>2022; 101018.<a id=\"_msocom_1\"><\/a><\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li><a id=\"_msocom_1\"><\/a>Leebeek FWG and Eikenboom JCJ. <em>N Engl J Med<\/em> 2016; 21:2067-80.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Srivastava A et al. <em>Haemophilia <\/em>2020; 26(Suppl 6):1-158.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Connell NT et al. <em>Blood Adv <\/em>2021; 5:301-25.<\/li>\n<\/div><\/ol>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>Von Willebrandova bolest (VWD) je naj\u010de\u0161\u0107i poreme\u0107aj krvarenja Kada je krvni sud povre\u0111en, deo crvenih krvnih zrnaca se slepljuje kako bi zatvorili ranu i zaustavili krvarenje. Taj se proces naziva zgru\u0161avanje. Kod osoba s poreme\u0107ajima krvarenja, kao \u0161to su VWD ili hemofilija, zgru\u0161avanje krvi ne funkcioni\u0161e pravilno. Zato su osobe s VWD-om sklonije \u010de\u0161\u0107em i [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":231,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"inline_featured_image":false},"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v20.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Saznajte vi\u0161e o von Willebrandovoj bolesti - Serbia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/vwdtest.com\/rs\/von-willebrand-disease\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Saznajte vi\u0161e o von Willebrandovoj bolesti - Serbia\" \/>\n<meta property=\"og:description\" content=\"Von Willebrandova bolest (VWD) je naj\u010de\u0161\u0107i poreme\u0107aj krvarenja Kada je krvni sud povre\u0111en, deo crvenih krvnih zrnaca se slepljuje kako bi zatvorili ranu i zaustavili krvarenje. Taj se proces naziva zgru\u0161avanje. Kod osoba s poreme\u0107ajima krvarenja, kao \u0161to su VWD ili hemofilija, zgru\u0161avanje krvi ne funkcioni\u0161e pravilno. 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Taj se proces naziva zgru\u0161avanje. Kod osoba s poreme\u0107ajima krvarenja, kao \u0161to su VWD ili hemofilija, zgru\u0161avanje krvi ne funkcioni\u0161e pravilno. 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