{"id":19,"date":"2023-02-13T13:51:56","date_gmt":"2023-02-13T13:51:56","guid":{"rendered":"https:\/\/new.vwdtest.com\/ro\/?page_id=19"},"modified":"2024-06-07T10:01:58","modified_gmt":"2024-06-07T10:01:58","slug":"von-willebrand-disease","status":"publish","type":"page","link":"https:\/\/vwdtest.com\/ro\/von-willebrand-disease\/","title":{"rendered":"Afl\u0103 mai multe despre Boala von Willebrand"},"content":{"rendered":"<div class=\"default-block container\">\n<h2><strong>Boala von Willebrand (VWD) este <br>cea mai frecvent\u0103 tulburare de s\u00e2ngerare<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<h5 class=\"bleeding-symptoms-title live\">Atunci c\u00e2nd un vas de s\u00e2nge este afectat, o parte dintre globulele ro\u0219ii din s\u00e2nge se adun\u0103 laolalt\u0103 pentru a \u00eenchide rana \u0219i pentru a opri s\u00e2ngerarea. Acest proces se nume\u0219te coagulare. La persoanele cu tulbur\u0103ri de s\u00e2ngerare, cum ar fi VWD sau hemofilia, coagularea s\u00e2ngelui nu func\u021bioneaz\u0103 corespunz\u0103tor. Prin urmare, persoanele cu VWD tind s\u0103 s\u00e2ngereze mai frecvent \u0219i pentru perioade mai \u00eendelungate, \u0219i se confrunt\u0103 cu <a href=\"https:\/\/vwdtest.com\/ro\/bleeding-symptoms\/#nosebleed\">s\u00e2nger\u0103ri nazale<\/a>, <a href=\"https:\/\/vwdtest.com\/ro\/bleeding-symptoms\/#oral-bleed\">s\u00e2nger\u0103ri gingivale<\/a> sau <a href=\"https:\/\/vwdtest.com\/ro\/bleeding-symptoms\/#minor-wounds\">s\u00e2nger\u0103ri dup\u0103 r\u0103ni minore<\/a>. Femeile cu VWD au adesea <a href=\"https:\/\/vwdtest.com\/ro\/bleeding-symptoms\/#hmb\">s\u00e2nger\u0103ri menstruale abundente<\/a>. La persoanele cu VWD, s\u00e2ngerarea este cauzat\u0103 de deficitul factorului von Willebrand (VWF), o protein\u0103 cu rol important \u00een coagularea s\u00e2ngelui.<sup>1<\/sup><\/h5>\n<\/div>\n\n<img decoding=\"async\" src=\"https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2023\/02\/hero2.webp\" alt=\"Afl\u0103 mai multe despre Boala von Willebrand\" class=\"page_thumbnail d-xl-none\">\r\n\n\n<div class=\"default-block container\">\n<figure class=\"is-layout-flex wp-block-gallery-1 wp-block-gallery has-nested-images columns-default is-cropped\"><div class=\"default-block container\">\n<figure class=\"wp-block-image size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"868\" height=\"484\" data-id=\"3183\"  src=\"https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2024\/04\/Illustration-01-1_ro.png\" alt=\"\" class=\"wp-image-3183\" srcset=\"https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2024\/04\/Illustration-01-1_ro.png 868w, https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2024\/04\/Illustration-01-1_ro-300x167.png 300w, https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2024\/04\/Illustration-01-1_ro-768x428.png 768w\" sizes=\"(max-width: 868px) 100vw, 868px\" \/><\/figure>\n<\/div><\/figure>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>Factorul von Willebrand (VWF) are un rol important \u00een coagularea s\u00e2ngelui<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VWF este o protein\u0103 care circul\u0103 prin s\u00e2nge. Este produs de celulele din vasele de s\u00e2nge \u0219i oase \u0219i eliberat \u00een fluxul sanguin. \u00cen cazul unei r\u0103ni, <strong>VWF lucreaz\u0103 \u00eempreun\u0103 cu alte proteine pentru a opri s\u00e2ngerarea prin formarea unui cheag de s\u00e2nge<\/strong>. La persoanele cu VWD, organismul nu produce suficient VWF sau proteina nu func\u021bioneaz\u0103 corect. Prin urmare, coagularea s\u00e2ngelui nu func\u021bioneaz\u0103 corespunz\u0103tor \u0219i s\u00e2ngerarea poate fi prelungit\u0103.<sup>2<\/sup><\/p>\n<\/div>\n\n\r\n\r\n<div class=\"styledBox\">\r\n    <h2 class=\"styledBox__title\">Exist\u0103 trei categorii principale de VWD<\/h2>\r\n\r\n    <ul class=\"styledBox__list\">\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD de Tip 1: <\/strong>Aproximativ 3 din 4 persoane cu VWD au VWD de Tip 1, aceasta fiind cea mai frecvent\u0103 form\u0103 a bolii. Aceste persoane au un nivel sc\u0103zut de protein\u0103 VWF.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD de TIP 2:<\/strong>\u00a0La persoanele cu VWD de Tip 2, proteina VWF nu func\u021bioneaz\u0103 corespunz\u0103tor.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD de Tip 3:<\/strong>\u00a0Este adesea o form\u0103 mai sever\u0103 a bolii, \u00een compara\u021bie cu VWD de Tip 1 \u0219i 2, \u0219i reprezint\u0103 cea mai rar\u0103 form\u0103 a acestei afec\u021biuni. Persoanele cu VWD de Tip 3 prezint\u0103 un nivel foarte sc\u0103zut de protein\u0103 VWF.<sup>2<\/sup><\/p>\n        <\/li>\r\n        <\/ul>\r\n<\/div>\n\n<div class=\"default-block container\">\n<h2>Care este diferen\u021ba \u00eentre VWD \u0219i hemofilie?<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">At\u00e2t VWD c\u00e2t \u0219i hemofilia sunt tulbur\u0103ri de s\u00e2ngerare. Persoanele cu oricare dintre cele dou\u0103 boli prezint\u0103 un risc mai mare de s\u00e2ngerare, dar p\u0103r\u021bile corpului \u00een care apare de obicei s\u00e2ngerarea sunt diferite la persoanele cu VWD fa\u021b\u0103 de cele cu hemofilie. Tulbur\u0103rile sunt cauzate de defecte ale diferitelor proteine: VWD este cauzat\u0103 de defecte ale proteinei VWF, \u00een timp ce hemofilia apare din cauza lipsei par\u021biale sau complete a proteinelor numite factor VIII \u0219i factor IX. Aceste cauze diferite \u00eenseamn\u0103 c\u0103 bolile au tratamente diferite.<sup>3,4<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>VWD poate fi tratat\u0103<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>Nu exist\u0103 vindecare a VWD, dar exist\u0103 <a href=\"https:\/\/vwdtest.com\/ro\/i-live-with-vwd\/\">tratamente eficiente<\/a>. Majoritatea persoanelor cu VWD au simptome foarte u\u0219oare, pe care le pot gestiona singuri \u00een via\u021ba lor de zi cu zi. Cu toate acestea, persoanele cu forme severe de VWD pot avea s\u00e2nger\u0103ri mai grave \u0219i mai frecvente, cu un impact mai mare asupra vie\u021bii lor.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p><strong>Dac\u0103 suferi de VWD, este important s\u0103 te \u00eenregistrezi la un <a href=\"https:\/\/vwdtest.com\/ro\/helpful-resources\/#region\">centru local de tratament<\/a> specializat \u00een tulbur\u0103ri de s\u00e2ngerare.<\/strong> Personalul de la centrul de tratament va raspunde tuturor \u00eentreb\u0103rilor tale \u0219i te va indruma \u00een gestionarea bolii, astfel \u00eenc\u00e2t s\u0103 po\u021bi duce o via\u021b\u0103 normal\u0103.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p>De asemenea, recomandarea noastr\u0103 este s\u0103 iei leg\u0103tura cu <a href=\"https:\/\/vwdtest.com\/ro\/helpful-resources\/#region\">asocia\u021biile locale de pacien\u021bi<\/a>. Exist\u0103 mai multe persoane cu tulbur\u0103ri de s\u00e2ngerare dec\u00e2t ai putea crede \u0219i vor fi bucuro\u0219i s\u0103 \u00eemp\u0103rt\u0103\u0219easc\u0103 cu tine experien\u021bele lor.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-5 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"259\" height=\"325\" src=\"https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2023\/02\/Illustration-03.png\" alt=\"\" class=\"wp-image-26\" srcset=\"https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2023\/02\/Illustration-03.png 259w, https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2023\/02\/Illustration-03-239x300.png 239w\" sizes=\"(max-width: 259px) 100vw, 259px\" \/><\/figure>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<h2>P\u00e2n\u0103 la 1% din popula\u021bia global\u0103 ar putea suferi de VWD<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>VWD este de obicei mo\u0219tenit\u0103 \u0219i afecteaz\u0103 at\u00e2t b\u0103rba\u021bii, c\u00e2t \u0219i femeile de toate v\u00e2rstele, inclusiv copiii. Simptomele apar mai frecvent \u00een r\u00e2ndul femeilor, acestea prezent\u00e2nd s\u00e2nger\u0103ri \u00een timpul menstrua\u021biei, sarcinii \u0219i na\u0219terii.<br><br><strong>Multe persoane au simptome u\u0219oare \u0219i este posibil s\u0103 nu realizeze c\u0103 au VWD. <\/strong><\/p>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-10 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-8 wp-block-columns\">\n<div class=\"is-layout-flow wp-block-column\"><div class=\"default-block container\">\n<h2>Adesea, persoanele cu VWD a\u0219teapt\u0103 mul\u021bi ani diagnosticul<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"orange\">Este adesea dificil de stabilit dac\u0103 s\u00e2ngerarea este normal\u0103 sau nu. \u00cen plus, multe persoane nu sunt con\u0219tiente de tulbur\u0103rile de s\u00e2ngerare, cum ar fi VWD. De aceea, persoanele cu VWD trebuie adesea s\u0103 a\u0219tepte c\u00e2\u021biva ani de la primele simptome de s\u00e2ngerare p\u00e2n\u0103 la diagnosticul final. Aceast\u0103 \u00eent\u00e2rziere este mai mare la femei dec\u00e2t la b\u0103rba\u021bi. <b>F\u0103r\u0103 diagnostic \u0219i tratament, pacien\u021bii pot suferi de s\u00e2nger\u0103ri frecvente, deficien\u021b\u0103 de fier, durere \u0219i sc\u0103derea calit\u0103\u021bii vie\u021bii.<\/b> Chiar dac\u0103 simptomele de s\u00e2ngerare sunt u\u0219oare \u00een via\u021ba de zi cu zi, exist\u0103 riscul de s\u00e2ngerare grav\u0103 \u00een timpul unei interven\u021bii chirurgicale sau ca urmare a unei accident\u0103ri<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p>De aceea, este<strong> important\u0103 con\u0219tientizarea simptomelor \u0219i a tulbur\u0103rilor de s\u00e2ngerare, a\u0219a cum este VWD<\/strong>.  Dac\u0103 ai \u00eengrijor\u0103ri legate de s\u00e2nger\u0103rile cu care te-ai confruntat, te rug\u0103m s\u0103 faci testul nostru de s\u00e2ngerare.<\/p>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full is-style-default\"><img decoding=\"async\" loading=\"lazy\" width=\"480\" height=\"331\" src=\"https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2023\/02\/Fill-47-1.png\" alt=\"\" class=\"wp-image-50\" srcset=\"https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2023\/02\/Fill-47-1.png 480w, https:\/\/vwdtest.com\/ro\/wp-content\/uploads\/sites\/53\/2023\/02\/Fill-47-1-300x207.png 300w\" sizes=\"(max-width: 480px) 100vw, 480px\" \/><\/figure>\n<\/div><\/div>\n<\/div>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<h2>Pentru diagnosticarea VWD sunt necesare istoricul s\u00e2nger\u0103rii \u0219i analize de laborator<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>VWD este o afec\u021biune rar\u0103 \u0219i nu to\u021bi medicii sunt familiariza\u021bi cu aceasta. Prin urmare, un <strong>diagnostic definitiv trebuie pus de un medic specializat \u00een tulbur\u0103ri de s\u00e2ngerare.<\/strong> Un diagnostic de VWD se stabile\u0219te \u00een urma unui proces. Ini\u021bial, medicul trebuie s\u0103 \u00een\u021beleag\u0103 orice s\u00e2ngerare cu care te confrun\u021bi tu \u0219i, eventual, al\u021bi membri ai familiei. Aceste informa\u021bii se numesc \u201eistoric de s\u00e2ngerare\u201d. Pentru a evalua istoricul complet de s\u00e2ngerare, medicul \u00ee\u021bi va pune o serie de \u00eentreb\u0103ri. Dac\u0103 istoricul de s\u00e2ngerare sugereaz\u0103 c\u0103 este posibil s\u0103 ai o tulburare de s\u00e2ngerare, va fi necesar\u0103 efectuarea unor analize de s\u00e2nge \u00eentr-un laborator specializat. Av\u00e2nd rezultatele analizelor, medicul va pune un diagnostic definitiv.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>Cu c\u00e2t prime\u0219ti diagnosticul mai devreme, cu at\u00e2t mai rapid vei putea face alegeri informate cu privire la tratament \u0219i stilul de via\u021b\u0103.<\/strong><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h6>Referin\u021be<\/h6>\n<\/div>\n\n<div class=\"default-block container\">\n<ol><div class=\"default-block container\">\n<li>Corrales-Medina FF et al. <em>Blood Rev <\/em>2022; 101018.<a id=\"_msocom_1\"><\/a><\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li><a id=\"_msocom_1\"><\/a>Leebeek FWG and Eikenboom JCJ. <em>N Engl J Med<\/em> 2016; 21:2067-80.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Srivastava A et al. <em>Haemophilia <\/em>2020; 26(Suppl 6):1-158.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Connell NT et al. <em>Blood Adv <\/em>2021; 5:301-25.<\/li>\n<\/div><\/ol>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>Boala von Willebrand (VWD) este cea mai frecvent\u0103 tulburare de s\u00e2ngerare Atunci c\u00e2nd un vas de s\u00e2nge este afectat, o parte dintre globulele ro\u0219ii din s\u00e2nge se adun\u0103 laolalt\u0103 pentru a \u00eenchide rana \u0219i pentru a opri s\u00e2ngerarea. Acest proces se nume\u0219te coagulare. La persoanele cu tulbur\u0103ri de s\u00e2ngerare, cum ar fi VWD sau hemofilia, [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":231,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"inline_featured_image":false},"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v20.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Afl\u0103 mai multe despre Boala von Willebrand - Romania<\/title>\n<meta name=\"robots\" content=\"noindex, follow\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Afl\u0103 mai multe despre Boala von Willebrand - Romania\" \/>\n<meta property=\"og:description\" content=\"Boala von Willebrand (VWD) este cea mai frecvent\u0103 tulburare de s\u00e2ngerare Atunci c\u00e2nd un vas de s\u00e2nge este afectat, o parte dintre globulele ro\u0219ii din s\u00e2nge se adun\u0103 laolalt\u0103 pentru a \u00eenchide rana \u0219i pentru a opri s\u00e2ngerarea. Acest proces se nume\u0219te coagulare. 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Acest proces se nume\u0219te coagulare. 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