{"id":19,"date":"2023-02-13T13:51:56","date_gmt":"2023-02-13T13:51:56","guid":{"rendered":"https:\/\/new.vwdtest.com\/lv\/?page_id=19"},"modified":"2026-04-08T13:01:39","modified_gmt":"2026-04-08T13:01:39","slug":"von-willebrand-disease","status":"publish","type":"page","link":"https:\/\/vwdtest.com\/lv\/von-willebrand-disease\/","title":{"rendered":"<strong>Uzzin\u0101t vair\u0101k par Villebranda slim\u012bbu<\/strong>"},"content":{"rendered":"<div class=\"default-block container\">\n<h2><strong><strong>Villebranda slim\u012bba (VS) ir bie\u017e\u0101k\u0101 asinsreces slim\u012bba<\/strong><\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<h5 class=\"bleeding-symptoms-title live\">Kad asinsvads tiek boj\u0101ts, da\u013ca sarkano asins \u0161\u016bnu sal\u012bp kop\u0101, lai aizv\u0113rtu br\u016bci un aptur\u0113tu asi\u0146o\u0161anu. \u0160o procesu sauc par asinsreci. Cilv\u0113kiem ar asinsreces trauc\u0113jumiem, piem\u0113ram, VS vai hemofiliju, asinsrece nenotiek pilnv\u0113rt\u012bgi. T\u0101d\u0113\u013c <strong>cilv\u0113kiem ar VS ir rakstur\u012bga bie\u017e\u0101ka un ilg\u0101ka asi\u0146o\u0161ana<\/strong>, piem\u0113ram, <a href=\"https:\/\/vwdtest.com\/lv\/bleeding-symptoms\/#nosebleed\">deguna asi\u0146o\u0161ana<\/a>, <a href=\"https:\/\/vwdtest.com\/lv\/bleeding-symptoms\/#oral-bleed\">smaganu asi\u0146o\u0161ana<\/a> vai asi\u0146o\u0161ana p\u0113c <a href=\"https:\/\/vwdtest.com\/lv\/bleeding-symptoms\/#minor-wounds\">neliel\u0101m traum\u0101m<\/a>. Sieviet\u0113m ar VS bie\u017ei ir <a href=\"https:\/\/vwdtest.com\/lv\/bleeding-symptoms\/#hmb\">stipra menstru\u0101l\u0101 asi\u0146o\u0161ana<\/a>. Cilv\u0113kiem ar VS asi\u0146o\u0161ana rodas asinsreces proces\u0101 noz\u012bm\u012bg\u0101 Villebranda faktora (VWF) prote\u012bna defektu d\u0113\u013c.<sup>1<\/sup><\/h5>\n<\/div>\n\n<div class=\"default-block container\">\n<figure class=\"is-layout-flex wp-block-gallery-1 wp-block-gallery has-nested-images columns-default is-cropped\"><div class=\"default-block container\">\n<figure class=\"wp-block-image size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"868\" height=\"484\" data-id=\"2967\"  src=\"https:\/\/vwdtest.com\/lv\/wp-content\/uploads\/sites\/76\/2026\/03\/74-1.png\" alt=\"\" class=\"wp-image-2967\" srcset=\"https:\/\/vwdtest.com\/lv\/wp-content\/uploads\/sites\/76\/2026\/03\/74-1.png 868w, https:\/\/vwdtest.com\/lv\/wp-content\/uploads\/sites\/76\/2026\/03\/74-1-300x167.png 300w, https:\/\/vwdtest.com\/lv\/wp-content\/uploads\/sites\/76\/2026\/03\/74-1-768x428.png 768w\" sizes=\"(max-width: 868px) 100vw, 868px\" \/><\/figure>\n<\/div><\/figure>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>Villebranda faktors (VWF) ir svar\u012bgs asinsreces proces\u0101<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VWF ir asin\u012bs cirkul\u0113jo\u0161s prote\u012bns. To sintez\u0113 asinsvadu un kaulu \u0161\u016bnas, un tas non\u0101k asinsrit\u0113. Traumas gad\u012bjum\u0101 <strong>VWF sadarbojas ar citiem prote\u012bniem, lai aptur\u0113tu asi\u0146o\u0161anu, veidojot asins recekli<\/strong>. Cilv\u0113kiem ar VS organism\u0101 neveidojas pietiekami daudz VWF vai prote\u012bns nedarbojas pareizi. Rezult\u0101t\u0101 nenotiek pilnv\u0113rt\u012bga asinsrece, un asi\u0146o\u0161ana var b\u016bt ilgsto\u0161a.<sup>2<\/sup><\/p>\n<\/div>\n\n\r\n\r\n<div class=\"styledBox\">\r\n    <h2 class=\"styledBox__title\">Ir tr\u012bs galvenie VS veidi<\/h2>\r\n\r\n    <ul class=\"styledBox__list\">\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>1.tipa VS: <\/strong>Aptuveni 3 no katriem 4 cilv\u0113kiem ar VS ir slim\u012bbas 1. tips, kas ir visizplat\u012bt\u0101kais \u0161\u012bs slim\u012bbas tips. \u0160iem cilv\u0113kiem ir zems VWF prote\u012bna l\u012bmenis.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>2. tipa VS:<\/strong> Cilv\u0113kiem ar 2. tipa VS ir VWF prote\u012bns, kas nedarbojas pareizi.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>3.tipa VS:<\/strong> \u0160\u012b slim\u012bbas forma ir visret\u0101k sastopama un bie\u017ei vien smag\u0101ka nek\u0101 1. vai 2. tipa slim\u012bba. Cilv\u0113kiem ar 3. tipa VS ir \u013coti zems VWF prote\u012bna l\u012bmenis.<sup>2<\/sup><\/p>\n        <\/li>\r\n        <\/ul>\r\n<\/div>\n\n<div class=\"default-block container\">\n<h2>K\u0101da ir at\u0161\u0137ir\u012bba starp VS un hemofiliju?<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Gan VS, gan hemofilija ir asinsreces slim\u012bbas. Abu slim\u012bbu gad\u012bjum\u0101 cilv\u0113kiem ir palielin\u0101ts asi\u0146o\u0161anas risks, bet \u0137erme\u0146a da\u013cas, kur\u0101s parasti rodas asi\u0146o\u0161ana, cilv\u0113kiem ar VS un hemofiliju ir at\u0161\u0137ir\u012bgas. Trauc\u0113jumus izraisa at\u0161\u0137ir\u012bgu prote\u012bnu defekti: VS izraisa VWF prote\u012bna defekti, bet hemofilija rodas t\u0101d\u0113\u013c, ka da\u013c\u0113ji tr\u016bkst vai nemaz nav prote\u012bnu, ko sauc par VIII un IX faktoru. \u0160ie da\u017e\u0101die c\u0113lo\u0146i noz\u012bm\u0113, ka slim\u012bb\u0101m ir at\u0161\u0137ir\u012bgas \u0101rst\u0113\u0161anas metodes.<sup>3,4<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong><strong>VS ir \u0101rst\u0113jama<\/strong><\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>VS nav iesp\u0113jams iz\u0101rst\u0113t, bet ir pieejami <a href=\"https:\/\/vwdtest.com\/lv\/i-live-with-vwd\/\">efekt\u012bvi \u0101rst\u0113\u0161anas l\u012bdzek\u013ci<\/a>. Liel\u0101kajai da\u013cai cilv\u0113ku ar VS ir \u013coti viegli simptomi, kurus vi\u0146i sav\u0101 ikdienas dz\u012bv\u0113 var nov\u0113rst pa\u0161i. Tom\u0113r cilv\u0113kiem ar smag\u0101m VS form\u0101m var b\u016bt smag\u0101ka un bie\u017e\u0101ka asi\u0146o\u0161ana, kas vair\u0101k ietekm\u0113 vi\u0146u dz\u012bvi.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p><strong>Ja <\/strong><strong>jums ir VS, ir svar\u012bgi re\u0123istr\u0113ties viet\u0113j\u0101 \u0101rst\u0113\u0161anas centr\u0101, kas specializ\u0113jas asinsreces trauc\u0113jumu \u0101rst\u0113\u0161an\u0101.<\/strong> <a href=\"https:\/\/vwdtest.com\/lv\/helpful-resources\/#region\">\u0100rst\u0113\u0161anas centra<\/a> person\u0101ls atbild\u0113s uz visiem j\u016bsu jaut\u0101jumiem un pal\u012bdz\u0113s jums tikt gal\u0101 ar slim\u012bbu, lai j\u016bs var\u0113tu dz\u012bvot norm\u0101lu dz\u012bvi. M\u0113s ar\u012b iesak\u0101m sazin\u0101ties ar viet\u0113j\u0101m<a href=\"https:\/\/vwdtest.com\/lv\/helpful-resources\/#region\"> pacientu asoci\u0101cij\u0101m<\/a>. Cilv\u0113ku ar asinsreces trauc\u0113jumiem ir vair\u0101k, nek\u0101 j\u016bs dom\u0101jat, un vi\u0146i labpr\u0101t dal\u012bsies ar jums sav\u0101 pieredz\u0113.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-5 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"259\" height=\"325\" src=\"https:\/\/vwdtest.com\/lv\/wp-content\/uploads\/sites\/76\/2023\/02\/Illustration-03.png\" alt=\"\" class=\"wp-image-26\" srcset=\"https:\/\/vwdtest.com\/lv\/wp-content\/uploads\/sites\/76\/2023\/02\/Illustration-03.png 259w, https:\/\/vwdtest.com\/lv\/wp-content\/uploads\/sites\/76\/2023\/02\/Illustration-03-239x300.png 239w\" sizes=\"(max-width: 259px) 100vw, 259px\" \/><\/figure>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<h2><strong>VS var b\u016bt l\u012bdz 1&nbsp;% pasaules iedz\u012bvot\u0101ju<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>VS parasti ir iedzimta un ar to slimo gan v\u012brie\u0161i, gan sievietes jebkur\u0101 vecum\u0101, tai skait\u0101 b\u0113rni. Sieviet\u0113m ir liel\u0101ka varb\u016bt\u012bba piedz\u012bvot VS simptomus nek\u0101 v\u012brie\u0161iem, jo menstru\u0101ciju, gr\u016btniec\u012bbas un dzemd\u012bbu laik\u0101 rodas asi\u0146o\u0161ana.<br><br><br><br><br><strong><strong>Daudziem cilv\u0113kiem simptomi ir viegli, un vi\u0146i neapzin\u0101s, ka vi\u0146iem ir VS.<\/strong><\/strong><\/p>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-10 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-8 wp-block-columns\">\n<div class=\"is-layout-flow wp-block-column\"><div class=\"default-block container\">\n<h2><strong><strong>Cilv\u0113kiem ar VS diagnoze bie\u017ei tiek noteikta p\u0113c daudziem gadiem<\/strong><\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"orange\">Bie\u017ei ir gr\u016bti pateikt, vai asi\u0146o\u0161ana ir norm\u0101la. Turkl\u0101t daudzi cilv\u0113ki nezina par t\u0101diem asinsreces trauc\u0113jumiem k\u0101 VS. \u0160o iemeslu d\u0113\u013c cilv\u0113kiem ar VS bie\u017ei vien j\u0101gaida vair\u0101kus gadus no pirmajiem asi\u0146o\u0161anas simptomiem l\u012bdz gal\u012bgajai diagnozei. Sieviet\u0113m \u0161\u012b kav\u0113\u0161an\u0101s parasti ir liel\u0101ka nek\u0101 v\u012brie\u0161iem. <b>Bez diagnozes un \u0101rst\u0113\u0161anas pacienti var ciest no bie\u017eas asi\u0146o\u0161anas, dzelzs defic\u012bta, s\u0101p\u0113m un dz\u012bves kvalit\u0101tes pasliktin\u0101\u0161an\u0101s. <\/b>Pat ja asi\u0146o\u0161anas simptomi ikdien\u0101 ir viegli, past\u0101v risks, ka oper\u0101cijas laik\u0101 vai p\u0113c negad\u012bjuma var rasties nopietna asi\u0146o\u0161ana.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p>T\u0101p\u0113c <strong>ir svar\u012bgi piev\u0113rst uzman\u012bbu asi\u0146o\u0161anas simptomiem un asisnreces trauc\u0113jumiem, piem\u0113ram, VS.<\/strong> Ja neesat p\u0101rliecin\u0101ts par savu asi\u0146o\u0161anu, l\u016bdzu, veiciet m\u016bsu asi\u0146o\u0161anas testu.<\/p>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full is-style-default\"><img decoding=\"async\" loading=\"lazy\" width=\"480\" height=\"331\" src=\"https:\/\/vwdtest.com\/lv\/wp-content\/uploads\/sites\/76\/2023\/02\/Fill-47-1.png\" alt=\"\" class=\"wp-image-50\" srcset=\"https:\/\/vwdtest.com\/lv\/wp-content\/uploads\/sites\/76\/2023\/02\/Fill-47-1.png 480w, https:\/\/vwdtest.com\/lv\/wp-content\/uploads\/sites\/76\/2023\/02\/Fill-47-1-300x207.png 300w\" sizes=\"(max-width: 480px) 100vw, 480px\" \/><\/figure>\n<\/div><\/div>\n<\/div>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong><strong>Lai diagnostic\u0113tu VS, ir nepiecie\u0161ama inform\u0101cija par asi\u0146o\u0161anas v\u0113sturi un laboratoriskas anal\u012bzes<\/strong><\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VS ir reta slim\u012bba, un ne visi \u0101rsti to atpaz\u012bst. T\u0101p\u0113c <strong>gal\u012bgo diagnozi j\u0101nosaka \u0101rstam, kas specializ\u0113jas asinsreces trauc\u0113jumu jom\u0101.<\/strong> VS diagnostika parasti ir process. S\u0101kum\u0101 \u0101rstam ir j\u0101izprot asi\u0146o\u0161anas epizodes, kas var b\u016bt biju\u0161as jums un, iesp\u0113jams, ar\u012b citiem j\u016bsu \u0123imenes locek\u013ciem. \u0160o inform\u0101ciju sauc par \u201casi\u0146o\u0161anas v\u0113sturi\u201d. Lai nov\u0113rt\u0113tu visu asi\u0146o\u0161anas v\u0113sturi, \u0101rsts jums uzdos virkni jaut\u0101jumu. Ja asi\u0146o\u0161anas v\u0113sture liecina, ka jums var\u0113tu b\u016bt asinsreces trauc\u0113jumi, j\u016bsu asinis ir j\u0101analiz\u0113 specializ\u0113t\u0101 laboratorij\u0101.<sup>1<\/sup> Pamatojoties uz asins anal\u012b\u017eu rezult\u0101tiem, \u0101rsts noteiks gal\u012bgo diagnozi.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong><strong>Jo \u0101tr\u0101k tiks noteikta diagnoze, jo \u0101tr\u0101k var\u0113siet s\u0101kt izdar\u012bt apzin\u0101tas izv\u0113les par \u0101rst\u0113\u0161anu un dz\u012bvesveidu.<\/strong><\/strong><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h6>Atsauces<\/h6>\n<\/div>\n\n<div class=\"default-block container\">\n<ol><div class=\"default-block container\">\n<li>Corrales-Medina FF et al. <em>Blood Rev <\/em>2022; 101018.<a id=\"_msocom_1\"><\/a><\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li><a id=\"_msocom_1\"><\/a>Leebeek FWG and Eikenboom JCJ. <em>N Engl J Med<\/em> 2016; 21:2067-80.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Srivastava A et al. <em>Haemophilia <\/em>2020; 26(Suppl 6):1-158.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Connell NT et al. <em>Blood Adv <\/em>2021; 5:301-25.<\/li>\n<\/div><\/ol>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>Villebranda slim\u012bba (VS) ir bie\u017e\u0101k\u0101 asinsreces slim\u012bba Kad asinsvads tiek boj\u0101ts, da\u013ca sarkano asins \u0161\u016bnu sal\u012bp kop\u0101, lai aizv\u0113rtu br\u016bci un aptur\u0113tu asi\u0146o\u0161anu. \u0160o procesu sauc par asinsreci. Cilv\u0113kiem ar asinsreces trauc\u0113jumiem, piem\u0113ram, VS vai hemofiliju, asinsrece nenotiek pilnv\u0113rt\u012bgi. T\u0101d\u0113\u013c cilv\u0113kiem ar VS ir rakstur\u012bga bie\u017e\u0101ka un ilg\u0101ka asi\u0146o\u0161ana, piem\u0113ram, deguna asi\u0146o\u0161ana, smaganu asi\u0146o\u0161ana vai [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":231,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"inline_featured_image":false},"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v20.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Uzzin\u0101t vair\u0101k par Villebranda slim\u012bbu - Latvia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/vwdtest.com\/lv\/von-willebrand-disease\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Uzzin\u0101t vair\u0101k par Villebranda slim\u012bbu - Latvia\" \/>\n<meta property=\"og:description\" content=\"Villebranda slim\u012bba (VS) ir bie\u017e\u0101k\u0101 asinsreces slim\u012bba Kad asinsvads tiek boj\u0101ts, da\u013ca sarkano asins \u0161\u016bnu sal\u012bp kop\u0101, lai aizv\u0113rtu br\u016bci un aptur\u0113tu asi\u0146o\u0161anu. \u0160o procesu sauc par asinsreci. Cilv\u0113kiem ar asinsreces trauc\u0113jumiem, piem\u0113ram, VS vai hemofiliju, asinsrece nenotiek pilnv\u0113rt\u012bgi. 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Cilv\u0113kiem ar asinsreces trauc\u0113jumiem, piem\u0113ram, VS vai hemofiliju, asinsrece nenotiek pilnv\u0113rt\u012bgi. 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