{"id":19,"date":"2023-02-13T13:51:56","date_gmt":"2023-02-13T13:51:56","guid":{"rendered":"https:\/\/new.vwdtest.com\/lt\/?page_id=19"},"modified":"2024-03-04T11:56:44","modified_gmt":"2024-03-04T11:56:44","slug":"von-willebrand-disease","status":"publish","type":"page","link":"https:\/\/vwdtest.com\/lt\/von-willebrand-disease\/","title":{"rendered":"Su\u017einokite daugiau apie von Willebrand lig\u0105"},"content":{"rendered":"<div class=\"default-block container\">\n<h2><strong>Von Willebrand liga (VWD) yra <br>da\u017eniausias kraujavimo sutrikimas<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<h5 class=\"bleeding-symptoms-title live\">Kai pa\u017eeid\u017eiama kraujagysl\u0117, kai kurie raudonieji kraujo k\u016bneliai sulimpa, kad u\u017edaryt\u0173 \u017eaizd\u0105 ir sustabdyt\u0173 kraujavim\u0105. \u0160is procesas vadinamas kre\u0161\u0117jimu. \u017dmon\u0117ms, turintiems kraujavimo sutrikim\u0173, toki\u0173 kaip VWD ar hemofilija, kraujo kre\u0161\u0117jimas neveikia tinkamai. Tod\u0117l <strong>\u017emon\u0117s, sergantys VWD, link\u0119 kraujuoti da\u017eniau ir ilgiau<\/strong>, pvz., <a href=\"https:\/\/vwdtest.com\/lt\/bleeding-symptoms\/#nosebleed\">kraujuoja i\u0161 nosies,<\/a><a href=\"https:\/\/vwdtest.com\/lt\/bleeding-symptoms\/#oral-bleed\"> danten\u0173 kraujavimas<\/a> arba po <a href=\"https:\/\/vwdtest.com\/lt\/bleeding-symptoms\/#minor-wounds\"> nesunk\u016bs su\u017ealojimai <\/a>. Moterys, sergan\u010dios VWD, da\u017enai patiria <a href=\"https:\/\/vwdtest.com\/lt\/bleeding-symptoms\/#hmb\"> gaus\u0173 menstruacin\u012f kraujavim\u0105<\/a>. \u017dmon\u0117ms, sergantiems VWD, kraujavim\u0105 sukelia fon Willebrand faktoriaus (VWF) baltymo, kuris yra svarbus kraujo kre\u0161\u0117jimui, defektai.<sup>1<\/sup><\/h5>\n<\/div>\n\n<img decoding=\"async\" src=\"https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/02\/hero2.webp\" alt=\"Su\u017einokite daugiau apie von Willebrand lig\u0105\" class=\"page_thumbnail d-xl-none\">\r\n\n\n<div class=\"default-block container\">\n<figure class=\"wp-block-image size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"1024\" height=\"510\" src=\"https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/03\/Illustration-01-1024x510-1.png\" alt=\"\" class=\"wp-image-323\" srcset=\"https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/03\/Illustration-01-1024x510-1.png 1024w, https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/03\/Illustration-01-1024x510-1-300x149.png 300w, https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/03\/Illustration-01-1024x510-1-768x383.png 768w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>Von Willebrand faktorius (VWF) yra svarbus kraujo kre\u0161\u0117jimui<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VWF yra kraujyje cirkuliuojantis baltymas. J\u012f gamina kraujagysli\u0173 ir kaul\u0173 l\u0105stel\u0117s ir patenka \u012f krauj\u0105. Su\u017ealojimo atveju <a class=\"orange-text\">VWF veikia kartu su kitais baltymais, kad sustabdyt\u0173 kraujavim\u0105, sudarydamas kraujo kre\u0161ul\u012f<\/a>. \u017dmoni\u0173, sergan\u010di\u0173 VWD, organizmas negamina pakankamai VWF arba baltymai neveikia tinkamai. D\u0117l to kraujo kre\u0161\u0117jimas neveikia tinkamai ir kraujavimas gali u\u017esit\u0119sti.<sup>2<\/sup><\/p>\n<\/div>\n\n\r\n\r\n<div class=\"styledBox\">\r\n    <h2 class=\"styledBox__title\">Yra trys pagrindiniai VWD tipai<\/h2>\r\n\r\n    <ul class=\"styledBox__list\">\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>1 tipo VWD: <\/strong>ma\u017edaug 3 i\u0161 4 \u017emoni\u0173, sergan\u010di\u0173 VWD, turi 1 tip\u0105, tod\u0117l tai yra labiausiai paplit\u0119s \u0161ios ligos tipas. \u0160ie \u017emon\u0117s turi ma\u017e\u0105 VWF baltymo kiek\u012f.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>2 tipo VWD:<\/strong> \u017emon\u0117s, sergantys 2 tipo VWD, turi VWF baltymo, kuris neveikia tinkamai.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>3 tipo VWD:<\/strong> da\u017enai sunkesn\u0117 nei 1 ar 2 tipo, tai yra re\u010diausia ligos forma. \u017dmoni\u0173, sergan\u010di\u0173 3 tipo VWD, VWF baltymo kiekis yra labai ma\u017eas.<sup>2<\/sup><\/p>\n        <\/li>\r\n        <\/ul>\r\n<\/div>\n\n<div class=\"default-block container\">\n<h2>Kuo skiriasi VWD ir hemofilija?<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Ir VWD, ir hemofilija yra kraujavimo sutrikimai. \u017dmon\u0117ms, sergantiems bet kuria liga, kraujavimo rizika yra didesn\u0117, ta\u010diau k\u016bno dalys, kuriose da\u017eniausiai kraujuoja, n\u0117ra vienodos \u017emon\u0117ms, sergantiems VWD ar hemofilija. Sutrikimus sukelia \u012fvairi\u0173 baltym\u0173 defektai: VWD sukelia VWF baltymo defektai, o hemofilija atsiranda d\u0117l dalinio arba visi\u0161ko baltym\u0173, vadinam\u0173 VIII ir IX faktoriumi, tr\u016bkumo. \u0160ios skirtingos prie\u017eastys rei\u0161kia, kad ligos gydomos skirtingai.<sup>3,4<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>VWD galima gydyti<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">N\u0117ra VWD gydymo, ta\u010diau yra <a href=\"\/lt\/i-live-with-vwd\">veiksming\u0173 gydymo b\u016bd\u0173<\/a>. Dauguma \u017emoni\u0173, sergan\u010di\u0173 VWD, turi labai lengvus simptomus, kuriuos jie gali valdyti patys kasdieniame gyvenime. Ta\u010diau \u017emon\u0117ms, sergantiems sunkiomis VWD formomis, kraujavimas gali b\u016bti sunkesnis ir da\u017enesnis, o tai gali tur\u0117ti didesn\u012f poveik\u012f j\u0173 gyvenimui.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>Jei sergate VWD, svarbu u\u017esiregistruoti vietiniame gydymo centre, kurio specializacija yra kraujavimo sutrikimai.<\/strong> <a href=\"\/lt\/helpful-resources\/\">gydymo \u012fstaigos darbuotojai centras<\/a> atsakys \u012f visus j\u016bs\u0173 klausimus ir pad\u0117s suvaldyti lig\u0105, kad gal\u0117tum\u0117te gyventi \u012fprast\u0105 gyvenim\u0105.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Taip pat rekomenduojame susisiekti su vietin\u0117mis <a href=\"\/lt\/helpful-resources\/\"> pacient\u0173 asociacijomis<\/a>. Kraujavimo sutrikim\u0173 turin\u010di\u0173 \u017emoni\u0173 yra daugiau, nei manote, ir jie mielai pasidalins su jumis savo patirtimi.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-3 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"259\" height=\"325\" src=\"https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/02\/Illustration-03.png\" alt=\"\" class=\"wp-image-26\" srcset=\"https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/02\/Illustration-03.png 259w, https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/02\/Illustration-03-239x300.png 239w\" sizes=\"(max-width: 259px) 100vw, 259px\" \/><\/figure>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<h2>Iki 1 % pasaulio gyventoj\u0173 gali sirgti VWD<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>VWD da\u017eniausiai yra paveldima ir serga \u012fvairaus am\u017eiaus vyrai ir moterys, \u012fskaitant vaikus. Moterims da\u017eniau pasirei\u0161kia VWD simptomai nei vyrams d\u0117l kraujavimo\n menstruacijos, n\u0117\u0161tumas ir gimdymas.<br><br><strong>Daugelis \u017emoni\u0173 turi lengv\u0173 simptom\u0173 ir gali nesuvokti, kad serga VWD.<\/strong><br><br><\/p>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-8 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-6 wp-block-columns\">\n<div class=\"is-layout-flow wp-block-column\"><div class=\"default-block container\">\n<h2><strong>\u017dmon\u0117s, sergantys VWD, da\u017enai laukia diagnoz\u0117s daugel\u012f met\u0173<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"orange\">Da\u017enai sunku pasakyti, ar kraujavimas normalus, ar ne. Be to, daugelis \u017emoni\u0173 ne\u017eino apie kraujavimo sutrikimus, tokius kaip VWD. D\u0117l \u0161i\u0173 prie\u017eas\u010di\u0173 VWD sergantiems \u017emon\u0117ms da\u017enai tenka laukti kelet\u0105 met\u0173 nuo pirm\u0173j\u0173 kraujavimo simptom\u0173 iki galutin\u0117s diagnoz\u0117s nustatymo. \u0160is v\u0117lavimas yra didesnis moterims nei vyrams. <strong>Nediagnozuojant ir negydant pacientai gali da\u017enai kraujuoti, tr\u016bkti gele\u017eies, patirti skausm\u0105 ir pablog\u0117ti gyvenimo kokyb\u0117. <\/strong>Net jei kraujavimo simptomai kasdieniame gyvenime yra lengvi, operacijos metu arba po nelaimingo atsitikimo kyla rimto kraujavimo pavojus.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p>Tod\u0117l<strong>,<mark style=\"background-color:rgba(0, 0, 0, 0)\" class=\"has-inline-color has- oran\u017ein\u0117s spalvos\"> <\/mark>svarbu \u017einoti apie kraujavimo simptomus ir kraujavimo sutrikimus, pvz., VWD<\/strong> . Jei nesate tikri d\u0117l bet kokio kraujavimo, atlikite kraujavimo test\u0105.<\/p>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full is-style-default\"><img decoding=\"async\" loading=\"lazy\" width=\"480\" height=\"331\" src=\"https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/02\/Fill-47-1.png\" alt=\"\" class=\"wp-image-50\" srcset=\"https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/02\/Fill-47-1.png 480w, https:\/\/vwdtest.com\/lt\/wp-content\/uploads\/sites\/15\/2023\/02\/Fill-47-1-300x207.png 300w\" sizes=\"(max-width: 480px) 100vw, 480px\" \/><\/figure>\n<\/div><\/div>\n<\/div>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>Norint diagnozuoti VWD, reikalinga kraujavimo istorija ir laboratoriniai tyrimai<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VWD yra retas ir ne kiekvienas gydytojas yra susipa\u017ein\u0119s su \u0161ia liga. Tod\u0117l <strong>galutin\u0119 diagnoz\u0119 tur\u0117t\u0173 nustatyti gydytojas, kurio specializacija yra kraujavimo sutrikimai<\/strong>. VWD diagnoz\u0117 visada yra procesas. I\u0161 prad\u017ei\u0173 j\u016bs\u0173 gydytojas turi suprasti bet kok\u012f kraujavim\u0105, kur\u012f gal\u0117jote patirti j\u016bs ir galb\u016bt kiti j\u016bs\u0173 \u0161eimos nariai. \u0160i informacija vadinama \u201ekraujavimo istorija\u201c. Nor\u0117dami \u012fvertinti vis\u0105 kraujavimo istorij\u0105, gydytojas u\u017eduos jums kelet\u0105 klausim\u0173. Jei kraujavimo istorija rodo, kad galite tur\u0117ti kraujavimo sutrikim\u0173, j\u016bs\u0173 krauj\u0105 reikia i\u0161tirti specializuotoje laboratorijoje.<sup>1<\/sup> Remdamasis kraujo tyrim\u0173 rezultatais, gydytojas nustatys galutin\u0119 diagnoz\u0119.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>Kuo anks\u010diau su\u017einosite diagnoz\u0119, tuo grei\u010diau gal\u0117site priimti pagr\u012fstus sprendimus d\u0117l gydymo ir gyvenimo b\u016bdo.<\/strong><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h6>Nuorodos<\/h6>\n<\/div>\n\n<div class=\"default-block container\">\n<ol><div class=\"default-block container\">\n<li>Corrales-Medina FF et al. <em>Blood Rev <\/em>2022; 101018.<a id=\"_msocom_1\"><\/a><\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li><a id=\"_msocom_1\"><\/a>Leebeek FWG and Eikenboom JCJ. <em>N Engl J Med<\/em> 2016; 21:2067-80.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Srivastava A et al. <em>Haemophilia <\/em>2020; 26(Suppl 6):1-158.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Connell NT et al. <em>Blood Adv <\/em>2021; 5:301-25.<\/li>\n<\/div><\/ol>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>Von Willebrand liga (VWD) yra da\u017eniausias kraujavimo sutrikimas Kai pa\u017eeid\u017eiama kraujagysl\u0117, kai kurie raudonieji kraujo k\u016bneliai sulimpa, kad u\u017edaryt\u0173 \u017eaizd\u0105 ir sustabdyt\u0173 kraujavim\u0105. \u0160is procesas vadinamas kre\u0161\u0117jimu. \u017dmon\u0117ms, turintiems kraujavimo sutrikim\u0173, toki\u0173 kaip VWD ar hemofilija, kraujo kre\u0161\u0117jimas neveikia tinkamai. Tod\u0117l \u017emon\u0117s, sergantys VWD, link\u0119 kraujuoti da\u017eniau ir ilgiau, pvz., kraujuoja i\u0161 nosies, danten\u0173 kraujavimas [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":231,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"inline_featured_image":false},"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v20.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Su\u017einokite daugiau apie von Willebrand lig\u0105 - Lithuania<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/vwdtest.com\/lt\/von-willebrand-disease\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Su\u017einokite daugiau apie von Willebrand lig\u0105 - Lithuania\" \/>\n<meta property=\"og:description\" content=\"Von Willebrand liga (VWD) yra da\u017eniausias kraujavimo sutrikimas Kai pa\u017eeid\u017eiama kraujagysl\u0117, kai kurie raudonieji kraujo k\u016bneliai sulimpa, kad u\u017edaryt\u0173 \u017eaizd\u0105 ir sustabdyt\u0173 kraujavim\u0105. \u0160is procesas vadinamas kre\u0161\u0117jimu. \u017dmon\u0117ms, turintiems kraujavimo sutrikim\u0173, toki\u0173 kaip VWD ar hemofilija, kraujo kre\u0161\u0117jimas neveikia tinkamai. 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