{"id":19,"date":"2023-02-13T13:51:56","date_gmt":"2023-02-13T13:51:56","guid":{"rendered":"https:\/\/new.vwdtest.com\/hu\/?page_id=19"},"modified":"2026-01-19T21:24:56","modified_gmt":"2026-01-19T21:24:56","slug":"von-willebrand-disease","status":"publish","type":"page","link":"https:\/\/vwdtest.com\/hu\/von-willebrand-disease\/","title":{"rendered":"Tudjon meg t\u00f6bbet a von Willebrand betegs\u00e9gr\u0151l"},"content":{"rendered":"<div class=\"default-block container\">\n<h2>A <strong>von Willebrand betegs\u00e9g (VWD) a leggyakoribb v\u00e9rz\u00e9si rendelleness\u00e9g <\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<h5 class=\"bleeding-symptoms-title live\">Amikor megs\u00e9r\u00fcl egy v\u00e9red\u00e9ny, a v\u00f6r\u00f6sv\u00e9rtestek egy r\u00e9sze \u00f6sszetapad, hogy z\u00e1rja a sebet \u00e9s meg\u00e1ll\u00edtsa a v\u00e9rz\u00e9st. Ezt a folyamatot alvad\u00e1snak nevezik.  V\u00e9rz\u00e9si rendelleness\u00e9gekben, pl. VWD-ben vagy hemof\u00edli\u00e1ban szendved\u0151 emberekn\u00e9l a v\u00e9ralvad\u00e1s nem m\u0171k\u00f6dik megfelel\u0151en. Ez\u00e9rt a VWD-ben szenved\u0151 emberek gyakrabban \u00e9s hosszabb ideig v\u00e9reznek, pl. <a href=\"https:\/\/vwdtest.com\/hu\/bleeding-symptoms\/#nosebleed\">orrv\u00e9rz\u00e9s<\/a>, <a href=\"https:\/\/vwdtest.com\/hu\/bleeding-symptoms\/#oral-bleed\">\u00ednyv\u00e9rz\u00e9s<\/a> eset\u00e9ben, <a href=\"https:\/\/vwdtest.com\/hu\/bleeding-symptoms\/#minor-wounds\"> kisebb s\u00e9r\u00fcl\u00e9sek ut\u00e1n<\/a>. A VWD-ben szenved\u0151 n\u0151k gyakran <a href=\"https:\/\/vwdtest.com\/hu\/bleeding-symptoms\/#hmb\"> s\u00falyosan er\u0151s  menstru\u00e1c\u00f3s v\u00e9rz\u00e9st<\/a> tapasztalnak. A VWD-beteg emberekn\u00e9l a v\u00e9rz\u00e9st a v\u00e9ralvad\u00e1sban fontos szerepet j\u00e1tsz\u00f3 von Willebrand faktor (VWF) feh\u00e9rje defektusai okozz\u00e1k.<sup>1<\/sup><\/h5>\n<\/div>\n\n<img decoding=\"async\" src=\"https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2023\/02\/hero2.webp\" alt=\"Tudjon meg t\u00f6bbet a von Willebrand betegs\u00e9gr\u0151l\" class=\"page_thumbnail d-xl-none\">\r\n\n\n<div class=\"default-block container\">\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" loading=\"lazy\" width=\"1024\" height=\"571\" src=\"https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2025\/12\/Kollagen-1024x571.jpg\" alt=\"\" class=\"wp-image-4022\" srcset=\"https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2025\/12\/Kollagen-1024x571.jpg 1024w, https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2025\/12\/Kollagen-300x167.jpg 300w, https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2025\/12\/Kollagen-768x428.jpg 768w, https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2025\/12\/Kollagen-1536x856.jpg 1536w, https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2025\/12\/Kollagen.jpg 1736w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n<\/div>\n\n<div class=\"default-block container\">\n<h2> <strong>A von Willebrand faktor (VWF) fontos szerepet j\u00e1tszik a v\u00e9ralvad\u00e1sban<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">A VWF egy  v\u00e9rben kering\u0151 feh\u00e9rjemolekula. Az erek \u00e9s a csontok sejtjei termelik \u00e9s a v\u00e9r\u00e1ramba ker\u00fcl.  S\u00e9r\u00fcl\u00e9s eset\u00e9n a  <strong>VWF m\u00e1s feh\u00e9rj\u00e9kkel egy\u00fctt v\u00e9rr\u00f6gk\u00e9pz\u00e9ssel meg\u00e1ll\u00edtja a v\u00e9rz\u00e9st.<\/strong> A VWD-ben szenved\u0151 emberekn\u00e9l a szervezet nem termel elegend\u0151 VWF-et, vagy a feh\u00e9rje nem m\u0171k\u00f6dik megfelel\u0151en. Ennek eredm\u00e9nyek\u00e9nt a v\u00e9ralvad\u00e1s nem megfelel\u0151 \u00e9s a v\u00e9rz\u00e9s elh\u00faz\u00f3dhat.<sup>2<\/sup><\/p>\n<\/div>\n\n\r\n\r\n<div class=\"styledBox\">\r\n    <h2 class=\"styledBox__title\">A VWD-nek h\u00e1rom f\u0151 t\u00edpusa k\u00fcl\u00f6nb\u00f6ztethet\u0151 meg <\/h2>\r\n\r\n    <ul class=\"styledBox__list\">\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>\u00a01-es t\u00edpus\u00fa VWD: <\/strong>A VWD-ben szenved\u0151 betegek\u00a0 75%-\u00e1nak 1-es t\u00edpus\u00fa VWD-je van, ez a leggyakrabban el\u0151fordul\u00f3 t\u00edpus.\u00a0 Ezekn\u00e9l az emberekn\u00e9l\u00a0 a VWF feh\u00e9rje szintje alacsony.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>2-es t\u00edpus\u00fa VWD:<\/strong> A 2-es t\u00edpus\u00fa VWD-ben szenved\u0151k VWF feh\u00e9rj\u00e9je nem m\u0171k\u00f6dik megfelel\u0151en.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>3-as t\u00edpus\u00fa VWD:<\/strong> Gyakran s\u00falyosabb, mint az 1-es vagy 2-es t\u00edpus\u00fa, ez a t\u00edpus a betegs\u00e9g legritk\u00e1bb form\u00e1ja. A 3-as t\u00edpus\u00fa VWD-ben szenved\u0151 embereknek nagyon alacsony a VWF feh\u00e9rje szintje.<sup>2<\/sup><\/p>\n        <\/li>\r\n        <\/ul>\r\n<\/div>\n\n<div class=\"default-block container\">\n<h2>Mi a k\u00fcl\u00f6nbs\u00e9g a VWD \u00e9s a hemof\u00edlia k\u00f6z\u00f6tt?<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Mind a VWD, mind a  hemof\u00edlia v\u00e9rz\u00e9ses rendelleness\u00e9g. Mindk\u00e9t betegs\u00e9gben nagyobb a v\u00e9rz\u00e9s kock\u00e1zata, de a v\u00e9rz\u00e9sek a test elt\u00e9r\u0151 helyein jelentkezhetnek a VWD-ben vagy hemof\u00edli\u00e1ban. A rendelleness\u00e9geket k\u00fcl\u00f6nb\u00f6z\u0151 feh\u00e9rj\u00e9k okozz\u00e1k: a VWD-t a VWF feh\u00e9rje hib\u00e1i,  a hemof\u00edli\u00e1t pedig a VIII. faktornak \u00e9s a IX. faktornak nevezett feh\u00e9rj\u00e9k r\u00e9szleges vagy teljes hi\u00e1nya okozza. Ezen k\u00fcl\u00f6nb\u00f6z\u0151s\u00e9gek miatt a betegs\u00e9gek kezel\u00e9se elt\u00e9r\u0151. <sup>3,4<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>A VWD kezelhet\u0151<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Az VWD nem gy\u00f3gy\u00edthat\u00f3, de <a href=\"https:\/\/vwdtest.com\/hu\/i-live-with-vwd\/\">hat\u00e9konyan kezelhet\u0151<\/a>. A legt\u00f6bb VWD-ben szenved\u0151nek nagyon enyhe t\u00fcnetei vannak, amelyet k\u00f6nnyen kezelnek a mindennapi \u00e9let\u00fckben  saj\u00e1t maguk is. Ugyanakkor a VWD s\u00falyos form\u00e1iban szenved\u0151knek er\u0151sebb \u00e9s gyakoribb v\u00e9rz\u00e9seik lehetnek, amely az \u00e9let\u00fcket jobban befoly\u00e1solja.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>Ha VWD-je van, speci\u00e1lis hematol\u00f3giai gondoz\u00f3k\u00f6zpontba kell j\u00e1rjon.<\/strong> A <a href=\"https:\/\/vwdtest.com\/hu\/helpful-resources\/#region\">gondoz\u00e1si k\u00f6zpont <\/a> szem\u00e9lyzete v\u00e1laszol minden k\u00e9rd\u00e9s\u00e9re  \u00e9s \u00fatmutat\u00e1sokkal szolg\u00e1l a betegs\u00e9g kezel\u00e9s\u00e9re, hogy \u00d6n norm\u00e1lis \u00e9letet \u00e9lhessen.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Azt is javasoljuk, hogy vegye fel a kapcsolatot a magyar<a href=\"https:\/\/vwdtest.com\/hu\/helpful-resources\/#region\"> betegszervezetekkel<\/a>. T\u00f6bb ember szenved v\u00e9rz\u00e9ses rendelleness\u00e9gben, mint gondoln\u00e1 \u00e9s \u00f6r\u00f6mmel megosztj\u00e1k \u00d6nnel a tapasztalataikat. <\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-3 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"259\" height=\"325\" src=\"https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2023\/02\/Illustration-03.png\" alt=\"\" class=\"wp-image-26\" srcset=\"https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2023\/02\/Illustration-03.png 259w, https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2023\/02\/Illustration-03-239x300.png 239w\" sizes=\"(max-width: 259px) 100vw, 259px\" \/><\/figure>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<h2>A vil\u00e1g n\u00e9pess\u00e9g\u00e9nek ak\u00e1r 1%-a is VWD beteg lehet  <\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>A VWD \u00e1ltal\u00e1ban \u00f6r\u00f6kletes betegs\u00e9g \u00e9s mind a f\u00e9rfiakat, mind a n\u0151ket \u00e9rintheti, b\u00e1rmely \u00e9letkorban, a gyermekkort is bele\u00e9rtve. A n\u0151k eset\u00e9ben a t\u00fcnetek nagyobb val\u00f3sz\u00edn\u0171s\u00e9ggel jelentkeznek, a menstru\u00e1ci\u00f3, a terhess\u00e9g \u00e9s a sz\u00fcl\u00e9s sor\u00e1n fell\u00e9p\u0151 v\u00e9rz\u00e9s miatt.<br><br><strong>Sok embernek enyhe t\u00fcnetei vannak \u00e9s \u00e9szre sem veszik, hogy VWD betegek.<\/strong><\/p>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-8 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-6 wp-block-columns\">\n<div class=\"is-layout-flow wp-block-column\"><div class=\"default-block container\">\n<h2><strong>A VWD-ben szenved\u0151k gyakran \u00e9veket v\u00e1rnak a diagn\u00f3zisra <\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"orange\">Gyakran neh\u00e9z meg\u00e1llap\u00edtani, hogy a v\u00e9rz\u00e9s norm\u00e1lis-e vagy sem. Sokan nem ismerik a v\u00e9rz\u00e9ses rendelleness\u00e9geket, p\u00e9ld\u00e1ul a VWD-t. Ezen okok miatt a VWD-ben szenved\u0151knek gyakran t\u00f6bb \u00e9vet kell v\u00e1rniuk az els\u0151 v\u00e9rz\u00e9ses t\u00fcnetek ut\u00e1n a v\u00e9gs\u0151 diagn\u00f3zisig. Ez a k\u00e9sedelem nagyobb a n\u0151kn\u00e9l, mint a f\u00e9rfiakn\u00e1l. <b>Diagn\u00f3zis \u00e9s kezel\u00e9s n\u00e9lk\u00fcl a betegekn\u00e9l gyakori lehet a v\u00e9rz\u00e9s \u00e9s vashi\u00e1ny alakulhat ki, f\u00e1jdalmakkal \u00e9s cs\u00f6kkent \u00e9letmin\u0151s\u00e9ggel kell \u00e9ljenek. <\/b>M\u00e9g akkor is fenn\u00e1ll a s\u00falyos v\u00e9rz\u00e9s kock\u00e1zata egy balesetben vagy m\u0171t\u00e9t sor\u00e1n, ha egy\u00e9bk\u00e9nt enyh\u00e9k a v\u00e9rz\u00e9s t\u00fcnetei a mindennapokban.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p>Ez\u00e9rt<strong> fontos, hogy megismerj\u00fck a v\u00e9rz\u00e9ses t\u00fcneteket \u00e9s a v\u00e9rz\u00e9ses rendelleness\u00e9geket, mint  amilyen a VWD is<\/strong>. Ha bizonytalan az \u00d6n \u00e1ltal tapasztalt v\u00e9rz\u00e9ssel kapcsolatosan, k\u00e9rj\u00fck, t\u00f6ltse ki a v\u00e9rz\u00e9sfelm\u00e9r\u0151 teszt\u00fcnket.<\/p>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full is-style-default\"><img decoding=\"async\" loading=\"lazy\" width=\"480\" height=\"331\" src=\"https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2023\/02\/Fill-47-1.png\" alt=\"\" class=\"wp-image-50\" srcset=\"https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2023\/02\/Fill-47-1.png 480w, https:\/\/vwdtest.com\/hu\/wp-content\/uploads\/sites\/63\/2023\/02\/Fill-47-1-300x207.png 300w\" sizes=\"(max-width: 480px) 100vw, 480px\" \/><\/figure>\n<\/div><\/div>\n<\/div>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>A VWD diagnosztiz\u00e1l\u00e1s\u00e1hoz a v\u00e9rz\u00e9ses esem\u00e9nyek ismerete \u00e9s laborat\u00f3riumi vizsg\u00e1latok sz\u00fcks\u00e9gesek <\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">A VWD ritka \u00e9s nem minden orvos ismeri fel a betegs\u00e9get. <strong> A v\u00e9gleges diagn\u00f3zist ez\u00e9rt hematol\u00f3gus szakorvosnak kell meg\u00e1llap\u00edtania<\/strong>. A VWD  diagn\u00f3zis fel\u00e1ll\u00edt\u00e1sa mindig egy folyamat. El\u0151sz\u00f6r is kezel\u0151orvos\u00e1nak ismernie kell minden v\u00e9rz\u00e9ses esem\u00e9nyt, amelyet vagy \u00d6n vagy esetleg m\u00e1s csal\u00e1dtagjai m\u00e1r \u00e1t\u00e9ltek. Ezt az inform\u00e1ci\u00f3t \u201cv\u00e9rz\u00e9ses el\u0151zm\u00e9nyeknek\u201d nevezik. Az el\u0151zm\u00e9nyek felm\u00e9r\u00e9s\u00e9hez orvosa egy sor k\u00e9rd\u00e9st fog feltenni. Ha az el\u0151zm\u00e9nyek arra utalnak, hogy \u00d6nnek v\u00e9rz\u00e9ses rendelleness\u00e9ge lehet, a v\u00e9rvizsg\u00e1latot speci\u00e1lis,  erre szakosodott laborat\u00f3riumban v\u00e9gzik el.<sup>1<\/sup> A v\u00e9rvizsg\u00e1latok eredm\u00e9nye alapj\u00e1n orvosa fel\u00e1ll\u00edtja a v\u00e9gleges diagn\u00f3zist.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>Min\u00e9l hamarabb \u00e1ll\u00edtj\u00e1k fel a diagn\u00f3zist, ann\u00e1l hamarabb tud \u00d6n is t\u00e1j\u00e9koz\u00f3dni a javasolt kezel\u00e9sekr\u0151l \u00e9s az \u00e9letm\u00f3dj\u00e1t is \u00e9rint\u0151 k\u00f6r\u00fclm\u00e9nyekr\u0151l.<\/strong><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h6>Irodalom<\/h6>\n<\/div>\n\n<div class=\"default-block container\">\n<ol><div class=\"default-block container\">\n<li>Corrales-Medina FF et al. <em>Blood Rev <\/em>2022; 101018.<a id=\"_msocom_1\"><\/a><\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li><a id=\"_msocom_1\"><\/a>Leebeek FWG and Eikenboom JCJ. <em>N Engl J Med<\/em> 2016; 21:2067-80.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Srivastava A et al. <em>Haemophilia <\/em>2020; 26(Suppl 6):1-158.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Connell NT et al. <em>Blood Adv <\/em>2021; 5:301-25.<\/li>\n<\/div><\/ol>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>A von Willebrand betegs\u00e9g (VWD) a leggyakoribb v\u00e9rz\u00e9si rendelleness\u00e9g Amikor megs\u00e9r\u00fcl egy v\u00e9red\u00e9ny, a v\u00f6r\u00f6sv\u00e9rtestek egy r\u00e9sze \u00f6sszetapad, hogy z\u00e1rja a sebet \u00e9s meg\u00e1ll\u00edtsa a v\u00e9rz\u00e9st. Ezt a folyamatot alvad\u00e1snak nevezik. V\u00e9rz\u00e9si rendelleness\u00e9gekben, pl. VWD-ben vagy hemof\u00edli\u00e1ban szendved\u0151 emberekn\u00e9l a v\u00e9ralvad\u00e1s nem m\u0171k\u00f6dik megfelel\u0151en. Ez\u00e9rt a VWD-ben szenved\u0151 emberek gyakrabban \u00e9s hosszabb ideig v\u00e9reznek, pl. [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":231,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"inline_featured_image":false},"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v20.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Tudjon meg t\u00f6bbet a von Willebrand betegs\u00e9gr\u0151l - Hungary<\/title>\n<meta name=\"robots\" content=\"noindex, follow\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Tudjon meg t\u00f6bbet a von Willebrand betegs\u00e9gr\u0151l - Hungary\" \/>\n<meta property=\"og:description\" content=\"A von Willebrand betegs\u00e9g (VWD) a leggyakoribb v\u00e9rz\u00e9si rendelleness\u00e9g Amikor megs\u00e9r\u00fcl egy v\u00e9red\u00e9ny, a v\u00f6r\u00f6sv\u00e9rtestek egy r\u00e9sze \u00f6sszetapad, hogy z\u00e1rja a sebet \u00e9s meg\u00e1ll\u00edtsa a v\u00e9rz\u00e9st. Ezt a folyamatot alvad\u00e1snak nevezik. V\u00e9rz\u00e9si rendelleness\u00e9gekben, pl. VWD-ben vagy hemof\u00edli\u00e1ban szendved\u0151 emberekn\u00e9l a v\u00e9ralvad\u00e1s nem m\u0171k\u00f6dik megfelel\u0151en. Ez\u00e9rt a VWD-ben szenved\u0151 emberek gyakrabban \u00e9s hosszabb ideig v\u00e9reznek, pl. 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