{"id":19,"date":"2023-02-13T13:51:56","date_gmt":"2023-02-13T13:51:56","guid":{"rendered":"https:\/\/new.vwdtest.com\/cz\/?page_id=19"},"modified":"2024-09-09T09:39:41","modified_gmt":"2024-09-09T09:39:41","slug":"von-willebrand-disease","status":"publish","type":"page","link":"https:\/\/vwdtest.com\/cz\/von-willebrand-disease\/","title":{"rendered":"Zjist\u011bte v\u00edce o von Willebrandov\u011b chorob\u011b"},"content":{"rendered":"<div class=\"default-block container\">\n<h2><strong>Von Willebrandova choroba (vWch) je <br>nej\u010dast\u011bj\u0161\u00ed krv\u00e1civou poruchou<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<h5 class=\"bleeding-symptoms-title live\">P\u0159i poran\u011bn\u00ed krevn\u00ed c\u00e9vy doch\u00e1z\u00ed k jej\u00ed kontrakci a aktivaci krevn\u00edch desti\u010dek a koagula\u010dn\u00edch faktor\u016f, tak aby se r\u00e1na uzav\u0159ela a krv\u00e1cen\u00ed zastavilo. Tento proces se naz\u00fdv\u00e1 sr\u00e1\u017een\u00ed krve. U lid\u00ed s krv\u00e1civ\u00fdmi poruchami, jako je vWch nebo hemofilie, sr\u00e1\u017een\u00ed krve nefunguje spr\u00e1vn\u011b. Proto <strong>lid\u00e9 s vWch maj\u00ed tendenci krv\u00e1cet \u010dast\u011bji a d\u00e9le<\/strong>, nap\u0159\u00edklad <a href=\"https:\/\/vwdtest.com\/cz\/bleeding-symptoms\/#nosebleed\">krv\u00e1cen\u00ed z nosu<\/a>, <a href=\"https:\/\/vwdtest.com\/cz\/bleeding-symptoms\/#oral-bleed\">krv\u00e1cen\u00ed d\u00e1sn\u00ed<\/a> nebo po <a href=\"https:\/\/vwdtest.com\/cz\/bleeding-symptoms\/#minor-wounds\">drobn\u00e9m poran\u011bn\u00ed <\/a>. \u017deny s vWch \u010dasto za\u017e\u00edvaj\u00ed <a href=\"https:\/\/vwdtest.com\/cz\/bleeding-symptoms\/#hmb\">siln\u00e9 menstrua\u010dn\u00ed krv\u00e1cen\u00ed<\/a>. U lid\u00ed s vWch je krv\u00e1cen\u00ed zp\u016fsobeno defekty proteinu von Willebrandova faktoru (VWF), kter\u00fd je d\u016fle\u017eit\u00fd pro sr\u00e1\u017een\u00ed krve.<\/h5>\n<\/div>\n\n<img decoding=\"async\" src=\"https:\/\/vwdtest.com\/cz\/wp-content\/uploads\/sites\/35\/2023\/02\/hero2.webp\" alt=\"Zjist\u011bte v\u00edce o von Willebrandov\u011b chorob\u011b\" class=\"page_thumbnail d-xl-none\">\r\n\n\n<div class=\"default-block container\">\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/vwdtest.com\/cz\/wp-content\/uploads\/sites\/35\/2024\/09\/vwdtest_addtionalmaterial-1.png\" alt=\"\"\/><\/figure>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>Von Willebrand\u016fv faktor (VWF) je d\u016fle\u017eit\u00fd pro sr\u00e1\u017een\u00ed krve<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VWF je protein, kter\u00fd cirkuluje v krvi. Je produkov\u00e1n hlavn\u011b v bu\u0148kami v c\u00e9v\u00e1ch a kostech a uvol\u0148ov\u00e1n do krevn\u00edho ob\u011bhu. V p\u0159\u00edpad\u011b poran\u011bn\u00ed <strong>VWF spolupracuje s dal\u0161\u00edmi proteiny na zastaven\u00ed krv\u00e1cen\u00ed vytvo\u0159en\u00edm krevn\u00ed sra\u017eeniny<\/strong>. U lid\u00ed s vWch t\u011blo neprodukuje dostatek VWF nebo protein nefunguje spr\u00e1vn\u011b. V d\u016fsledku toho sr\u00e1\u017een\u00ed krve nefunguje spr\u00e1vn\u011b a krv\u00e1cen\u00ed se m\u016f\u017ee prodlou\u017eit.<\/p>\n<\/div>\n\n\r\n\r\n<div class=\"styledBox\">\r\n    <h2 class=\"styledBox__title\">Existuj\u00ed t\u0159i hlavn\u00ed typy VWD<\/h2>\r\n\r\n    <ul class=\"styledBox__list\">\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD typu 1: <\/strong>Asi 3 ze 4 osob s vWch maj\u00ed typ 1, co\u017e z n\u011bj \u010din\u00ed nej\u010dast\u011bj\u0161\u00ed typ onemocn\u011bn\u00ed. Tito lid\u00e9 maj\u00ed n\u00edzk\u00e9 hladiny proteinu VWF.<\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD typu 2:<\/strong> U osob s VWD typu 2 nefunguje VWF spr\u00e1vn\u011b.<\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD typu 3:<\/strong> Toto je nejvz\u00e1cn\u011bj\u0161\u00ed forma onemocn\u011bn\u00ed, kter\u00e1 je \u010dasto z\u00e1va\u017en\u011bj\u0161\u00ed ne\u017e typ 1 nebo 2. Lid\u00e9 s vWch typu 3 maj\u00ed velmi n\u00edzk\u00e9 hladiny proteinu VWF.<\/p>\n        <\/li>\r\n        <\/ul>\r\n<\/div>\n\n<div class=\"default-block container\">\n<h2>Jak\u00fd je rozd\u00edl mezi vWch a hemofili\u00ed?<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Jak vWch, tak hemofilie jsou krv\u00e1civ\u00e9 poruchy. Lid\u00e9 s ob\u011bma chorobami maj\u00ed vy\u0161\u0161\u00ed riziko krv\u00e1cen\u00ed, ale lokalita krv\u00e1cen\u00ed se li\u0161\u00ed u osob s vWch a hemofili\u00ed. Poruchy jsou zp\u016fsobeny defekty v r\u016fzn\u00fdch proteinech: vWch je zp\u016fsobena nedostatkem nebo defekty v proteinu VWF, zat\u00edmco hemofilie se vyskytuje v d\u016fsledku \u010d\u00e1ste\u010dn\u00e9ho nebo \u00fapln\u00e9ho nedostatku protein\u016f naz\u00fdvan\u00fdch faktor VIII a faktor IX. Tyto r\u016fzn\u00e9 p\u0159\u00ed\u010diny znamenaj\u00ed, \u017ee se nemoci l\u00e9\u010d\u00ed r\u016fzn\u011b.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h2>V<strong>Wch lze l\u00e9\u010dit<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VWch nelze trvale vyl\u00e9\u010dit , ale existuj\u00ed r\u016fzn\u00e9 <a href=\"https:\/\/vwdtest.com\/cz\/i-live-with-vwd\/\">\u00fa\u010dinn\u00e9 zp\u016fsoby l\u00e9\u010dby<\/a>. V\u011bt\u0161ina lid\u00ed s vWch m\u00e1 velmi m\u00edrn\u00e9 p\u0159\u00edznaky, kter\u00e9 mohou zvl\u00e1dnout sami ve sv\u00e9m ka\u017edodenn\u00edm \u017eivot\u011b. Lid\u00e9 s t\u011b\u017ek\u00fdmi formami vWch v\u0161ak mohou m\u00edt z\u00e1va\u017en\u011bj\u0161\u00ed a \u010dast\u011bj\u0161\u00ed krv\u00e1cen\u00ed s v\u011bt\u0161\u00edm dopadem na jejich kvalitu \u017eivota.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>Pokud m\u00e1te vWch, je d\u016fle\u017eit\u00e9, abyste se zaregistrovali v m\u00edstn\u00edm l\u00e9\u010debn\u00e9m centru, kter\u00e9 se specializuje na poruchy krv\u00e1cen\u00ed.<\/strong> Person\u00e1l <a href=\"https:\/\/vwdtest.com\/cz\/helpful-resources\/\">l\u00e9\u010debn\u00e9ho centra<\/a> zodpov\u00ed v\u0161echny va\u0161e ot\u00e1zky a povede v\u00e1s p\u0159i zvl\u00e1d\u00e1n\u00ed nemoci, abyste mohli \u017e\u00edt norm\u00e1ln\u00ed \u017eivot.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Doporu\u010dujeme tak\u00e9 kontaktovat m\u00edstn\u00ed <a href=\"https:\/\/vwdtest.com\/cz\/helpful-resources\/\">sdru\u017een\u00ed pacient\u016f<\/a>. Lid\u00ed s poruchami krv\u00e1cen\u00ed je v\u00edce, ne\u017e si mysl\u00edte, a r\u00e1di se s v\u00e1mi pod\u011bl\u00ed o sv\u00e9 zku\u0161enosti.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-3 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"259\" height=\"325\" src=\"https:\/\/vwdtest.com\/cz\/wp-content\/uploads\/sites\/35\/2023\/02\/Illustration-03.png\" alt=\"\" class=\"wp-image-26\" srcset=\"https:\/\/vwdtest.com\/cz\/wp-content\/uploads\/sites\/35\/2023\/02\/Illustration-03.png 259w, https:\/\/vwdtest.com\/cz\/wp-content\/uploads\/sites\/35\/2023\/02\/Illustration-03-239x300.png 239w\" sizes=\"(max-width: 259px) 100vw, 259px\" \/><\/figure>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<h2>A\u017e 1 % sv\u011btov\u00e9 populace m\u016f\u017ee m\u00edt vWch<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>vWch se obvykle d\u011bd\u00ed a postihuje mu\u017ee i \u017eeny v\u0161ech v\u011bkov\u00fdch kategori\u00ed, v\u010detn\u011b d\u011bt\u00ed. \u017deny \u010dast\u011bji vykazuj\u00ed p\u0159\u00edznaky vWch ne\u017e mu\u017ei kv\u016fli krv\u00e1cen\u00ed, ke kter\u00e9mu doch\u00e1z\u00ed p\u0159i menstruaci, t\u011bhotenstv\u00ed a porodu.<br><br><strong>Mnoho lid\u00ed m\u00e1 m\u00edrn\u00e9 p\u0159\u00edznaky a nemus\u00ed si uv\u011bdomit, \u017ee maj\u00ed vWch.<\/strong><br><br><\/p>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-8 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-6 wp-block-columns\">\n<div class=\"is-layout-flow wp-block-column\"><div class=\"default-block container\">\n<h2><strong>Lid\u00e9 s vWch<\/strong> <strong>\u010dasto \u010dekaj\u00ed na svou diagn\u00f3zu mnoho let<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>\u010casto je obt\u00ed\u017en\u00e9 ur\u010dit, zda je krv\u00e1cen\u00ed norm\u00e1ln\u00ed nebo ne. Nav\u00edc si mnoho lid\u00ed neuv\u011bdomuje, \u017ee p\u0159\u00ed\u010dinou nadm\u011brn\u00e9ho krv\u00e1cen\u00ed m\u016f\u017ee b\u00fdt vWch. Z t\u011bchto d\u016fvod\u016f mus\u00ed lid\u00e9 s vWch \u010dasto \u010dekat n\u011bkolik let od prvn\u00edch p\u0159\u00edznak\u016f krv\u00e1cen\u00ed do kone\u010dn\u00e9 diagn\u00f3zy. Toto zpo\u017ed\u011bn\u00ed je v\u011bt\u0161\u00ed u \u017een ne\u017e u mu\u017e\u016f. <strong>Bez diagn\u00f3zy a l\u00e9\u010dby mohou pacienti trp\u011bt \u010dast\u00fdm krv\u00e1cen\u00edm, nedostatkem \u017eeleza, bolest\u00ed a sn\u00ed\u017eenou kvalitou \u017eivota. <\/strong>I kdy\u017e jsou p\u0159\u00edznaky krv\u00e1cen\u00ed v ka\u017edodenn\u00edm \u017eivot\u011b m\u00edrn\u00e9, existuje riziko v\u00e1\u017en\u00e9ho krv\u00e1cen\u00ed b\u011bhem operace nebo po zran\u011bn\u00ed.\n<\/div>\n\n<div class=\"default-block container\">\n<p>Proto <strong>je d\u016fle\u017eit\u00e9 si uv\u011bdomovat krv\u00e1civ\u00e9 p\u0159\u00edznaky a krv\u00e1civ\u00e9 poruchy, jako je vWch.<\/strong> Pokud si nejste jisti krv\u00e1cen\u00edm, kter\u00e9 jste zaznamenali, ud\u011blejte si pros\u00edm n\u00e1\u0161 test krv\u00e1cen\u00ed.<\/p>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full is-style-default\"><img decoding=\"async\" loading=\"lazy\" width=\"480\" height=\"331\" src=\"https:\/\/vwdtest.com\/cz\/wp-content\/uploads\/sites\/35\/2023\/02\/Fill-47-1.png\" alt=\"\" class=\"wp-image-50\" srcset=\"https:\/\/vwdtest.com\/cz\/wp-content\/uploads\/sites\/35\/2023\/02\/Fill-47-1.png 480w, https:\/\/vwdtest.com\/cz\/wp-content\/uploads\/sites\/35\/2023\/02\/Fill-47-1-300x207.png 300w\" sizes=\"(max-width: 480px) 100vw, 480px\" \/><\/figure>\n<\/div><\/div>\n<\/div>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>K diagnostice vWch je zapot\u0159eb\u00ed anamn\u00e9za krv\u00e1cen\u00ed a laboratorn\u00ed testy<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">vWch je vz\u00e1cn\u00e9 onemocn\u011bn\u00ed a ne ka\u017ed\u00fd l\u00e9ka\u0159 je s touto nemoc\u00ed dostate\u010dn\u011b obezn\u00e1men. Proto by m<strong>\u011bl stanovit definitivn\u00ed diagn\u00f3zu l\u00e9ka\u0159, kter\u00fd se specializuje na poruchy krevn\u00ed sr\u00e1\u017elivosti<\/strong>. Diagn\u00f3za vWch je v\u017edy proces. Zpo\u010d\u00e1tku mus\u00ed v\u00e1\u0161 l\u00e9ka\u0159 porozum\u011bt jak\u00e9mukoli krv\u00e1cen\u00ed, kter\u00e9 jste vy a mo\u017en\u00e1 i dal\u0161\u00ed \u010dlenov\u00e9 va\u0161\u00ed rodiny mohli za\u017e\u00edt. Tato informace se naz\u00fdv\u00e1 anamn\u00e9za krv\u00e1cen\u00ed (\u201ehistorie krv\u00e1cen\u00ed\u201c). K posouzen\u00ed kompletn\u00ed anamn\u00e9zy krv\u00e1cen\u00ed v\u00e1m l\u00e9ka\u0159 polo\u017e\u00ed \u0159adu ot\u00e1zek. Pokud anamn\u00e9za krv\u00e1cen\u00ed nazna\u010duje, \u017ee byste mohli m\u00edt poruchu krevn\u00edho sr\u00e1\u017een\u00ed, je t\u0159eba va\u0161i krev analyzovat ve specializovan\u00e9 laborato\u0159i. Na z\u00e1klad\u011b v\u00fdsledk\u016f krevn\u00edch test\u016f stanov\u00ed v\u00e1\u0161 l\u00e9ka\u0159 definitivn\u00ed diagn\u00f3zu. <\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p><\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>Von Willebrandova choroba (vWch) je nej\u010dast\u011bj\u0161\u00ed krv\u00e1civou poruchou P\u0159i poran\u011bn\u00ed krevn\u00ed c\u00e9vy doch\u00e1z\u00ed k jej\u00ed kontrakci a aktivaci krevn\u00edch desti\u010dek a koagula\u010dn\u00edch faktor\u016f, tak aby se r\u00e1na uzav\u0159ela a krv\u00e1cen\u00ed zastavilo. Tento proces se naz\u00fdv\u00e1 sr\u00e1\u017een\u00ed krve. U lid\u00ed s krv\u00e1civ\u00fdmi poruchami, jako je vWch nebo hemofilie, sr\u00e1\u017een\u00ed krve nefunguje spr\u00e1vn\u011b. Proto lid\u00e9 s vWch [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":231,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"inline_featured_image":false},"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v20.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Zjist\u011bte v\u00edce o von Willebrandov\u011b chorob\u011b - Czech Republic<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/vwdtest.com\/cz\/von-willebrand-disease\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Zjist\u011bte v\u00edce o von Willebrandov\u011b chorob\u011b - Czech Republic\" \/>\n<meta property=\"og:description\" content=\"Von Willebrandova choroba (vWch) je nej\u010dast\u011bj\u0161\u00ed krv\u00e1civou poruchou P\u0159i poran\u011bn\u00ed krevn\u00ed c\u00e9vy doch\u00e1z\u00ed k jej\u00ed kontrakci a aktivaci krevn\u00edch desti\u010dek a koagula\u010dn\u00edch faktor\u016f, tak aby se r\u00e1na uzav\u0159ela a krv\u00e1cen\u00ed zastavilo. Tento proces se naz\u00fdv\u00e1 sr\u00e1\u017een\u00ed krve. U lid\u00ed s krv\u00e1civ\u00fdmi poruchami, jako je vWch nebo hemofilie, sr\u00e1\u017een\u00ed krve nefunguje spr\u00e1vn\u011b. 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