{"id":19,"date":"2023-02-13T13:51:56","date_gmt":"2023-02-13T13:51:56","guid":{"rendered":"https:\/\/new.vwdtest.com\/nw\/?page_id=19"},"modified":"2024-02-28T05:55:12","modified_gmt":"2024-02-28T05:55:12","slug":"von-willebrand-disease","status":"publish","type":"page","link":"https:\/\/vwdtest.com\/bkp-hu\/von-willebrand-disease\/","title":{"rendered":"Learn more about von willebrand disease"},"content":{"rendered":"<div class=\"default-block container\">\n<h2>A von Willebrand-k\u00f3r (VWD) az<br>a leggyakoribb v\u00e9rz\u00e9si rendelleness\u00e9g<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<h5 class=\"bleeding-symptoms-title live\">Ha egy \u00e9r megs\u00e9r\u00fcl, a v\u00f6r\u00f6sv\u00e9rtestek egy r\u00e9sze \u00f6sszetapad, hogy lez\u00e1rja a sebet \u00e9s meg\u00e1ll\u00edtsa a v\u00e9rz\u00e9st. Ezt a folyamatot v\u00e9ralvad\u00e1snak nevezik. V\u00e9rz\u00e9si rendelleness\u00e9gben, p\u00e9ld\u00e1ul VWD-ben vagy hemof\u00edli\u00e1ban szenved\u0151 betegekn\u00e9l a v\u00e9ralvad\u00e1s nem m\u0171k\u00f6dik megfelel\u0151en. Ez\u00e9rt <strong>a VWD-ben szenved\u0151k gyakrabban \u00e9s hosszabb ideig v\u00e9reznek<\/strong>, p\u00e9ld\u00e1ul <a href=\"https:\/\/vwdtest.com\/bkp-hu\/bleeding-symptoms\/#nosebleed\">orrv\u00e9rz\u00e9s<\/a>, <a href=\"https:\/\/vwdtest.com\/bkp-hu\/bleeding-symptoms\/#oral-bleed\">\u00ednyv\u00e9rz\u00e9s<\/a>, vagy <a href=\"https:\/\/vwdtest.com\/bkp-hu\/bleeding-symptoms\/#minor-wounds\"> kisebb s\u00e9r\u00fcl\u00e9sek <\/a>. A VWD-ben szenved\u0151 n\u0151k gyakran <a href=\"https:\/\/vwdtest.com\/bkp-hu\/bleeding-symptoms\/#hmb\">er\u0151s menstru\u00e1ci\u00f3s v\u00e9rz\u00e9st<\/a> tapasztalnak. VWD-s betegekn\u00e9l a v\u00e9rz\u00e9st a von Willebrand-faktor (VWF) feh\u00e9rje hib\u00e1ja okozza, amely fontos a v\u00e9ralvad\u00e1shoz.<sup>1<\/sup><\/h5>\n<\/div>\n\n<img decoding=\"async\" src=\"https:\/\/vwdtest.com\/bkp-hu\/wp-content\/uploads\/sites\/62\/2023\/02\/hero2.webp\" alt=\"Learn more about von willebrand disease\" class=\"page_thumbnail d-xl-none\">\r\n\n\n<div class=\"default-block container\">\n<figure class=\"is-layout-flex wp-block-gallery-1 wp-block-gallery has-nested-images columns-default is-cropped\"><div class=\"default-block container\">\n<figure class=\"wp-block-image size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"868\" height=\"484\" data-id=\"1569\"  src=\"https:\/\/vwdtest.com\/nw\/wp-content\/uploads\/sites\/62\/2023\/09\/Illustration-01-1.png\" alt=\"\" class=\"wp-image-1569\" srcset=\"https:\/\/vwdtest.com\/bkp-hu\/wp-content\/uploads\/sites\/62\/2023\/09\/Illustration-01-1.png 868w, https:\/\/vwdtest.com\/bkp-hu\/wp-content\/uploads\/sites\/62\/2023\/09\/Illustration-01-1-300x167.png 300w, https:\/\/vwdtest.com\/bkp-hu\/wp-content\/uploads\/sites\/62\/2023\/09\/Illustration-01-1-768x428.png 768w\" sizes=\"(max-width: 868px) 100vw, 868px\" \/><\/figure>\n<\/div><\/figure>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>A von Willebrand faktor (VWF) fontos a v\u00e9ralvad\u00e1shoz<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">A VWF egy feh\u00e9rje, amely a v\u00e9rben kering. Az erekben \u00e9s a csontokban l\u00e9v\u0151 sejtek termelik, \u00e9s a v\u00e9r\u00e1ramba ker\u00fclnek. S\u00e9r\u00fcl\u00e9s eset\u00e9n a<strong>VWF m\u00e1s feh\u00e9rj\u00e9kkel egy\u00fcttm\u0171k\u00f6dve v\u00e9rr\u00f6g k\u00e9pz\u0151d\u00e9s\u00e9vel meg\u00e1ll\u00edtja a v\u00e9rz\u00e9st<\/strong>. VWD-ben szenved\u0151kn\u00e9l a szervezet nem termel elegend\u0151 VWF-et, vagy a feh\u00e9rje nem m\u0171k\u00f6dik megfelel\u0151en. Ennek eredm\u00e9nyek\u00e9nt a v\u00e9ralvad\u00e1s nem m\u0171k\u00f6dik megfelel\u0151en, \u00e9s a v\u00e9rz\u00e9s elh\u00faz\u00f3dhat.<sup>2<\/sup><\/p>\n<\/div>\n\n\r\n\r\n<div class=\"styledBox\">\r\n    <h2 class=\"styledBox__title\">A VWD-nek h\u00e1rom f\u0151 t\u00edpusa van<\/h2>\r\n\r\n    <ul class=\"styledBox__list\">\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>1-es t\u00edpus\u00fa VWD: <\/strong>4 VWD-ben szenved\u0151 emberb\u0151l k\u00f6r\u00fclbel\u00fcl 3-nak van 1-es t\u00edpusa, \u00edgy ez a betegs\u00e9g leggyakoribb t\u00edpusa. Ezeknek az embereknek alacsony a VWF feh\u00e9rje szintje.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>2-es t\u00edpus\u00fa VWD:<\/strong> A 2-es t\u00edpus\u00fa VWD-ben szenved\u0151k VWF-feh\u00e9rj\u00e9je nem m\u0171k\u00f6dik megfelel\u0151en.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>3-as t\u00edpus\u00fa VWD:<\/strong> gyakran s\u00falyosabb, mint az 1. vagy 2. t\u00edpus\u00fa, ez a betegs\u00e9g legritk\u00e1bb form\u00e1ja. A 3-as t\u00edpus\u00fa VWD-ben szenved\u0151knek nagyon alacsony a VWF-feh\u00e9rje szintje.<sup>2<\/sup><\/p>\n        <\/li>\r\n        <\/ul>\r\n<\/div>\n\n<div class=\"default-block container\">\n<h2>Mi a k\u00fcl\u00f6nbs\u00e9g a VWD \u00e9s a hemof\u00edlia k\u00f6z\u00f6tt?<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Mind a VWD, mind a hemof\u00edlia v\u00e9rz\u00e9si rendelleness\u00e9g. B\u00e1rmelyik betegs\u00e9gben szenved\u0151kn\u00e9l nagyobb a v\u00e9rz\u00e9s kock\u00e1zata, de a test azon r\u00e9szei, ahol \u00e1ltal\u00e1ban v\u00e9rz\u00e9s fordul el\u0151, nem ugyanazok a VWD-ben vagy hemof\u00edli\u00e1ban szenved\u0151kn\u00e9l. A rendelleness\u00e9geket k\u00fcl\u00f6nb\u00f6z\u0151 feh\u00e9rj\u00e9k hib\u00e1i okozz\u00e1k: a VWD-t a VWF feh\u00e9rje hib\u00e1i okozz\u00e1k, m\u00edg a hemof\u00edli\u00e1t a VIII-as \u00e9s IX-es faktornak nevezett feh\u00e9rj\u00e9k r\u00e9szleges vagy teljes hi\u00e1nya okozza. Ezek a k\u00fcl\u00f6nb\u00f6z\u0151 okok azt jelentik, hogy a betegs\u00e9gek elt\u00e9r\u0151 kezel\u00e9st kapnak.<sup>3,4<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>A VWD kezelhet\u0151<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">A VWD-re nincs gy\u00f3gym\u00f3d, de vannak <a href=\"https:\/\/vwdtest.com\/bkp-hu\/i-live-with-vwd\/\">hat\u00e9kony kezel\u00e9sek<\/a>. A legt\u00f6bb VWD-ben szenved\u0151 embernek nagyon enyhe t\u00fcnetei vannak, amelyeket mindennapi \u00e9let\u00fck sor\u00e1n saj\u00e1t maguk kezelhetnek. A VWD s\u00falyos form\u00e1iban szenved\u0151knek azonban s\u00falyosabb \u00e9s gyakoribb v\u00e9rz\u00e9sei lehetnek, ami nagyobb hat\u00e1ssal lehet az \u00e9let\u00fckre.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>Ha VWD-je van, fontos, hogy regisztr\u00e1ljon egy v\u00e9rz\u00e9si rendelleness\u00e9gekre szakosodott helyi kezel\u0151k\u00f6zpontban.<\/strong> A <a href=\"https:\/\/vwdtest.com\/bkp-hu\/helpful-resources\/\">kezel\u0151k\u00f6zpont<\/a> minden k\u00e9rd\u00e9s\u00e9re v\u00e1laszt ad, \u00e9s eligaz\u00edtja a betegs\u00e9g kezel\u00e9s\u00e9ben, hogy norm\u00e1lis \u00e9letet \u00e9lhessen.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Javasoljuk tov\u00e1bb\u00e1, hogy vegye fel a kapcsolatot a helyi<a href=\"https:\/\/vwdtest.com\/bkp-hu\/helpful-resources\/\"> betegegyes\u00fcletekkel<\/a>. T\u00f6bb v\u00e9rz\u00e9si rendelleness\u00e9ggel k\u00fczd\u0151 ember van, mint gondoln\u00e1, \u00e9s sz\u00edvesen megosztj\u00e1k \u00d6nnel tapasztalataikat.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-5 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"259\" height=\"325\" src=\"https:\/\/vwdtest.com\/nw\/wp-content\/uploads\/sites\/62\/2023\/02\/Illustration-03.png\" alt=\"\" class=\"wp-image-26\" srcset=\"https:\/\/vwdtest.com\/bkp-hu\/wp-content\/uploads\/sites\/62\/2023\/02\/Illustration-03.png 259w, https:\/\/vwdtest.com\/bkp-hu\/wp-content\/uploads\/sites\/62\/2023\/02\/Illustration-03-239x300.png 239w\" sizes=\"(max-width: 259px) 100vw, 259px\" \/><\/figure>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<h2>A vil\u00e1g lakoss\u00e1g\u00e1nak legfeljebb 1%-a szenvedhet VWD-t<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>A VWD \u00e1ltal\u00e1ban \u00f6r\u00f6kl\u0151dik, \u00e9s mind a f\u00e9rfiakat, mind a n\u0151ket \u00e9rinti minden \u00e9letkorban, bele\u00e9rtve a gyermekeket is. A n\u0151k nagyobb val\u00f3sz\u00edn\u0171s\u00e9ggel mutatnak VWD-t\u00fcneteket, mint a f\u00e9rfiak a v\u00e9rz\u00e9s miatt\n menstru\u00e1ci\u00f3, terhess\u00e9g \u00e9s sz\u00fcl\u00e9s.<br><br><strong>Sok embernek enyhe t\u00fcnetei vannak, \u00e9s el\u0151fordulhat, hogy nem veszik \u00e9szre, hogy VWD-je van.<\/strong><\/p>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-10 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-8 wp-block-columns\">\n<div class=\"is-layout-flow wp-block-column\"><div class=\"default-block container\">\n<h2><strong>A VWD-ben szenved\u0151k gyakran \u00e9vekig v\u00e1rnak a diagn\u00f3zisra<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"orange\">Gyakran neh\u00e9z megmondani, hogy a v\u00e9rz\u00e9s norm\u00e1lis-e vagy sem. R\u00e1ad\u00e1sul sokan nincsenek tiszt\u00e1ban olyan v\u00e9rz\u00e9si rendelleness\u00e9gekkel, mint p\u00e9ld\u00e1ul a VWD. Ezen okok miatt a VWD-ben szenved\u0151knek gyakran t\u00f6bb \u00e9vet kell v\u00e1rniuk az els\u0151 v\u00e9rz\u00e9ses t\u00fcnetek megjelen\u00e9s\u00e9t\u0151l a v\u00e9gs\u0151 diagn\u00f3zisig. Ez a k\u00e9s\u00e9s nagyobb a n\u0151kn\u00e9l, mint a f\u00e9rfiakn\u00e1l. <b>Diagnosztika \u00e9s kezel\u00e9s hi\u00e1ny\u00e1ban a betegek gyakori v\u00e9rz\u00e9st\u0151l, vashi\u00e1nyt\u00f3l, f\u00e1jdalomt\u00f3l \u00e9s \u00e9letmin\u0151s\u00e9g roml\u00e1st\u00f3l szenvedhetnek. <\/b>M\u00e9g akkor is, ha a v\u00e9rz\u00e9ses t\u00fcnetek enyh\u00e9k a mindennapi \u00e9letben, fenn\u00e1ll a s\u00falyos v\u00e9rz\u00e9s vesz\u00e9lye m\u0171t\u00e9t k\u00f6zben vagy balesetet k\u00f6vet\u0151en.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p>Ez\u00e9rt<mark style=\"background-color:rgba(0, 0, 0, 0)\" class=\"has-inline-color has-orange-color\"> <\/mark><strong>fontos hogy tiszt\u00e1ban legyen a v\u00e9rz\u00e9ses t\u00fcnetekkel \u00e9s v\u00e9rz\u00e9si rendelleness\u00e9gekkel, mint p\u00e9ld\u00e1ul a VWD<\/strong>vel. Ha nem biztos abban, hogy b\u00e1rmilyen v\u00e9rz\u00e9st tapasztalt, k\u00e9rj\u00fck, v\u00e9gezze el v\u00e9rz\u00e9si teszt\u00fcnket.<\/p>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full is-style-default\"><img decoding=\"async\" loading=\"lazy\" width=\"480\" height=\"331\" src=\"https:\/\/vwdtest.com\/nw\/wp-content\/uploads\/sites\/62\/2023\/02\/Fill-47-1.png\" alt=\"\" class=\"wp-image-50\" srcset=\"https:\/\/vwdtest.com\/bkp-hu\/wp-content\/uploads\/sites\/62\/2023\/02\/Fill-47-1.png 480w, https:\/\/vwdtest.com\/bkp-hu\/wp-content\/uploads\/sites\/62\/2023\/02\/Fill-47-1-300x207.png 300w\" sizes=\"(max-width: 480px) 100vw, 480px\" \/><\/figure>\n<\/div><\/div>\n<\/div>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>A VWD diagnosztiz\u00e1l\u00e1s\u00e1hoz v\u00e9rz\u00e9st\u00f6rt\u00e9net \u00e9s laborat\u00f3riumi vizsg\u00e1latok sz\u00fcks\u00e9gesek<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">A VWD ritka, \u00e9s nem minden orvos ismeri a betegs\u00e9get. Ez\u00e9rt<strong>a v\u00e9gleges diagn\u00f3zist v\u00e9rz\u00e9si rendelleness\u00e9gekre szakosodott orvosnak kell fel\u00e1ll\u00edtania<\/strong>. A VWD diagn\u00f3zisa mindig folyamat. Kezdetben orvos\u00e1nak tudnia kell minden olyan v\u00e9rz\u00e9st, amelyet \u00d6n \u00e9s esetleg csal\u00e1dja m\u00e1s tagjai tapasztaltak. Ezt az inform\u00e1ci\u00f3t \u201ev\u00e9rz\u00e9st\u00f6rt\u00e9netnek\u201d nevezik. A teljes v\u00e9rz\u00e9st\u00f6rt\u00e9net felm\u00e9r\u00e9s\u00e9hez orvosa k\u00e9rd\u00e9seket fog feltenni. Ha a v\u00e9rz\u00e9ses anamn\u00e9zis arra utal, hogy v\u00e9rz\u00e9si rendelleness\u00e9ge lehet, v\u00e9r\u00e9t speci\u00e1lis laborat\u00f3riumban kell elemezni.<sup>1<\/sup> A v\u00e9rvizsg\u00e1latok eredm\u00e9nyei alapj\u00e1n kezel\u0151orvosa v\u00e9gleges diagn\u00f3zist \u00e1ll\u00edt fel.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>Min\u00e9l hamarabb diagnosztiz\u00e1lja, ann\u00e1l hamarabb kezdhet megalapozott d\u00f6nt\u00e9seket hozni kezel\u00e9s\u00e9vel \u00e9s \u00e9letm\u00f3dj\u00e1val kapcsolatban.<\/strong><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h6>Hivatkoz\u00e1sok<\/h6>\n<\/div>\n\n<div class=\"default-block container\">\n<ol><div class=\"default-block container\">\n<li>Corrales-Medina FF et al. Blood Rev 2022; 101018.<a id=\"_msocom_1\"><\/a><\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li><a id=\"_msocom_1\"><\/a>Leebeek FWG \u00e9s Eikenboom JCJ. N Engl J Med 2016; 21:2067-80.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Srivastava A et al. Haemophilia 2020; 26 (6. mell\u00e9klet): 1-158.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Connell NT et al. Blood Adv 2021; 5:301-25.<\/li>\n<\/div><\/ol>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>A von Willebrand-k\u00f3r (VWD) aza leggyakoribb v\u00e9rz\u00e9si rendelleness\u00e9g Ha egy \u00e9r megs\u00e9r\u00fcl, a v\u00f6r\u00f6sv\u00e9rtestek egy r\u00e9sze \u00f6sszetapad, hogy lez\u00e1rja a sebet \u00e9s meg\u00e1ll\u00edtsa a v\u00e9rz\u00e9st. Ezt a folyamatot v\u00e9ralvad\u00e1snak nevezik. V\u00e9rz\u00e9si rendelleness\u00e9gben, p\u00e9ld\u00e1ul VWD-ben vagy hemof\u00edli\u00e1ban szenved\u0151 betegekn\u00e9l a v\u00e9ralvad\u00e1s nem m\u0171k\u00f6dik megfelel\u0151en. Ez\u00e9rt a VWD-ben szenved\u0151k gyakrabban \u00e9s hosszabb ideig v\u00e9reznek, p\u00e9ld\u00e1ul orrv\u00e9rz\u00e9s, \u00ednyv\u00e9rz\u00e9s, [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":231,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"inline_featured_image":false},"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v20.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Learn more about von willebrand disease - Backup Hungry<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/vwdtest.com\/bkp-hu\/von-willebrand-disease\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Learn more about von willebrand disease - Backup Hungry\" \/>\n<meta property=\"og:description\" content=\"A von Willebrand-k\u00f3r (VWD) aza leggyakoribb v\u00e9rz\u00e9si rendelleness\u00e9g Ha egy \u00e9r megs\u00e9r\u00fcl, a v\u00f6r\u00f6sv\u00e9rtestek egy r\u00e9sze \u00f6sszetapad, hogy lez\u00e1rja a sebet \u00e9s meg\u00e1ll\u00edtsa a v\u00e9rz\u00e9st. Ezt a folyamatot v\u00e9ralvad\u00e1snak nevezik. V\u00e9rz\u00e9si rendelleness\u00e9gben, p\u00e9ld\u00e1ul VWD-ben vagy hemof\u00edli\u00e1ban szenved\u0151 betegekn\u00e9l a v\u00e9ralvad\u00e1s nem m\u0171k\u00f6dik megfelel\u0151en. 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