{"id":19,"date":"2023-02-13T13:51:56","date_gmt":"2023-02-13T13:51:56","guid":{"rendered":"https:\/\/new.vwdtest.com\/bo\/?page_id=19"},"modified":"2025-09-26T11:52:04","modified_gmt":"2025-09-26T11:52:04","slug":"von-willebrand-disease","status":"publish","type":"page","link":"https:\/\/vwdtest.com\/ba\/von-willebrand-disease\/","title":{"rendered":"Saznajte vi\u0161e o von Willebrandovoj bolesti"},"content":{"rendered":"<div class=\"default-block container\">\n<h2><strong>Von Willebrandova bolest (VWD) je <br>naj\u010de\u0161\u0107i poreme\u0107aj krvarenja<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<h5 class=\"bleeding-symptoms-title live\">Kada je krvna \u017eila povrije\u0111ena, dio crvenih krvnih \u0107elija se sljepljuje kako bi zatvorile ranu i zaustavile krvarenje. Taj se proces naziva zgru\u0161avanje. Kod osoba s poreme\u0107ajima krvarenja, kao \u0161to su VWB ili hemofilija, zgru\u0161avanje krvi ne funkcioni\u0161e pravilno. Zato su <strong>osobe s VWD-om sklonije \u010de\u0161\u0107em i dugotrajnijem krvarenju<\/strong>, na primjer <a href=\"https:\/\/vwdtest.com\/ba\/bleeding-symptoms\/#nosebleed\">krvarenju iz nosa<\/a>, <a href=\"https:\/\/vwdtest.com\/ba\/bleeding-symptoms\/#oral-bleed\">krvarenju desni<\/a> ili nakon<a href=\"https:\/\/vwdtest.com\/ba\/bleeding-symptoms\/#minor-wounds\"> manje povrede <\/a>. \u017dene s VWD-om \u010desto imaju <a href=\"https:\/\/vwdtest.com\/ba\/bleeding-symptoms\/#hmb\">obilno menstrualno krvarenje<\/a>. Kod osoba s VWD-om krvarenje je uzrokovano nedostatkom proteina von Willebrandovog faktora (VWF), koji je va\u017ean za zgru\u0161avanje krvi.<sup>1<\/sup><\/h5>\n<\/div>\n\n<img decoding=\"async\" src=\"https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/02\/hero2.webp\" alt=\"Saznajte vi\u0161e o von Willebrandovoj bolesti\" class=\"page_thumbnail d-xl-none\">\r\n\n\n<div class=\"default-block container\">\n<figure class=\"wp-block-image size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"1024\" height=\"510\" src=\"https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/03\/Illustration-01-1024x510-1.png\" alt=\"\" class=\"wp-image-323\" srcset=\"https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/03\/Illustration-01-1024x510-1.png 1024w, https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/03\/Illustration-01-1024x510-1-300x149.png 300w, https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/03\/Illustration-01-1024x510-1-768x383.png 768w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>Von Willebrandov faktor (VWF) va\u017ean je za zgru\u0161avanje krvi<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VWF je protein koji cirkuli\u0161e u krvi. Proizvode ga \u0107elije u krvnim \u017eilama i kostima i otpu\u0161taju ga u krvotok. U slu\u010daju povrede, <strong>VWF zajedno s drugim proteinima radi na zaustavljanju krvarenja stvaranjem krvnog ugru\u0161ka<\/strong>. Kod osoba s VWD-om tijelo ne proizvodi dovoljno VWF-a ili protein ne funkcioni\u0161e pravilno. Uslijed toga ni zgru\u0161avanje krvi ne funkcioni\u0161e pravilno i krvarenje mo\u017ee biti dugotrajnije.<sup>2<\/sup><\/p>\n<\/div>\n\n\r\n\r\n<div class=\"styledBox\">\r\n    <h2 class=\"styledBox__title\">Postoje tri glavne vrste VWD-a<\/h2>\r\n\r\n    <ul class=\"styledBox__list\">\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD tip 1: <\/strong>Otprilike 3 od 4 osobe s VWD-om pate od tipa 1, \u0161to ga \u010dini naj\u010de\u0161\u0107im tipom bolesti. Te osobe imaju niske razine proteina VWF.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD tip 2:<\/strong> Kod osoba s VWD-om tipa 2 VWF protein ne radi pravilno.<sup>2<\/sup><\/p>\n        <\/li>\r\n            <li class=\"styledBox__item\">\r\n            <p><strong>VWD tip 3:<\/strong> \u010cesto je te\u017ei od tipa 1 ili 2, a radi se o najrje\u0111em obliku ove bolesti. Osobe s VWD-om tipa 3 imaju vrlo niske razine proteina VWF.<sup>2<\/sup><\/p>\n        <\/li>\r\n        <\/ul>\r\n<\/div>\n\n<div class=\"default-block container\">\n<h2>Koja je razlika izme\u0111u VWD-a i hemofilije?<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">I VWD i hemofilija su poreme\u0107aji krvarenja. Osobe koje pate od obje bolesti imaju pove\u0107an rizik krvarenja, no kod osoba s VWD-om i osoba s hemofilijom do krvarenja obi\u010dno ne dolazi na istim dijelovima tijela. Ti su poreme\u0107aji uzrokovani nedostatkom razli\u010ditih proteina: VWD je uzrokovan nedostatkom proteina VWF, dok hemofilija nastaje zbog djelimi\u010dnog ili potpunog nedostatka proteina koji se nazivaju faktor VIII i faktor IX. Ovi razli\u010diti uzroci ukazuju i na razli\u010dite na\u010dine lije\u010denja bolesti.<sup>3,4<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>VWD se mo\u017ee lije\u010diti<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Ne postoji lijek za VWD, no postoje <a href=\"https:\/\/vwdtest.com\/ba\/i-live-with-vwd\/\">djelotvorne terapije<\/a>. Osobe s VWD-om ve\u0107inom imaju vrlo blage simptome s kojima se mogu sami nositi u svakodnevnom \u017eivotu. Me\u0111utim, osobe s te\u0161kim oblicima VWD-a mogu imati ozbiljnija i \u010de\u0161\u0107a krvarenja, s ve\u0107im uticajem na \u017eivot.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>Ako imate VWD, va\u017eno je da se prijavite u lokalnom centru za lije\u010denje koji je specijaliziran za poreme\u0107aje krvarenja.<\/strong> Osoblje u <a href=\"https:\/\/vwdtest.com\/ba\/helpful-resources\/\">centru za lije\u010denje<\/a> odgovorit \u0107e na sva Va\u0161a pitanja i voditi vas u zbrinjavanju bolesti kako biste mogli \u017eivjeti normalnim \u017eivotom.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">Uz to Vam savjetujemo da stupite u kontakt s lokalnim <a href=\"https:\/\/vwdtest.com\/ba\/helpful-resources\/\"> udru\u017eenjima pacijenata<\/a>. Ima vi\u0161e ljudi s poreme\u0107ajima krvarenja nego \u0161to mislite i rado \u0107e s Vama podijeliti svoja iskustva.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-3 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"259\" height=\"325\" src=\"https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/02\/Illustration-03.png\" alt=\"\" class=\"wp-image-26\" srcset=\"https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/02\/Illustration-03.png 259w, https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/02\/Illustration-03-239x300.png 239w\" sizes=\"(max-width: 259px) 100vw, 259px\" \/><\/figure>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<h2>Mogu\u0107e je da od VWD-a pati do 1% svjetske populacije<\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>VWD je u pravilu nasljedna bolest koja poga\u0111a i mu\u0161karce i \u017eene svake dobi, uklju\u010duju\u0107i djecu. Kod \u017eena je vjerojatnost nastanka simptoma VWD-a ve\u0107a nego kod mu\u0161karaca zbog krvarenja koje se javlja tijekom  menstruacije, trudno\u0107e i poroda.<br><br><strong>Mnogi ljudi imaju blage simptome i mo\u017eda ni ne znaju da imaju VWD.<\/strong><br><br><\/p>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-8 wp-block-columns are-vertically-aligned-center\">\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<div class=\"is-layout-flex wp-container-6 wp-block-columns\">\n<div class=\"is-layout-flow wp-block-column\"><div class=\"default-block container\">\n<h2><strong>Osobe s VWD-om \u010desto <strong>godinama<\/strong><\/strong> <strong>\u010dekaju  dijagnozu<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p>\u010cesto je te\u0161ko utvrditi je li krvarenje normalno. \u0160tavi\u0161e, mnogi ljudi nisu ni svjesni poreme\u0107aja krvarenja kao \u0161to je VWD. Zato osobe s VWD-om \u010desto moraju \u010dekati i nekoliko godina od prvih simptoma krvarenja do kona\u010dne dijagnoze. Pritom pacijentice \u010dekaju du\u017ee od pacijenata. <strong>Bez dijagnoze i lije\u010denja pacijenti mogu patiti od \u010destih krvarenja, nedostatka \u017eeljeza, bolova i smanjene kvalitete \u017eivota. <\/strong>\u010cak i ako su simptomi krvarenja u svakodnevnom \u017eivotu blagi, postoji rizik od ozbiljnog krvarenja tijekom operacije ili nakon nezgode.<sup>1<\/sup><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p>Zato<strong> je<mark style=\"background-color:rgba(0, 0, 0, 0)\" class=\"has-inline-color has- naran\u010dasta boja\"> <\/mark>va\u017eno je biti svjestan simptoma krvarenja i poreme\u0107aja krvarenja kao \u0161to je VWD.<\/strong> Ako ste u nedoumici u vezi bilo kojeg krvarenja, ispunite na\u0161 test krvarenja.<\/p>\n<\/div><\/div>\n\n\n\n<div class=\"is-layout-flow wp-block-column is-vertically-aligned-center\"><div class=\"default-block container\">\n<figure class=\"wp-block-image aligncenter size-full is-style-default\"><img decoding=\"async\" loading=\"lazy\" width=\"480\" height=\"331\" src=\"https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/02\/Fill-47-1.png\" alt=\"\" class=\"wp-image-50\" srcset=\"https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/02\/Fill-47-1.png 480w, https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/02\/Fill-47-1-300x207.png 300w\" sizes=\"(max-width: 480px) 100vw, 480px\" \/><\/figure>\n<\/div><\/div>\n<\/div>\n<\/div><\/div>\n<\/div>\n<\/div>\n\n<div class=\"default-block container\">\n<h2><strong>Za dijagnosticiranje VWD-a potrebni su historija krvarenja i laboratorijske pretrage<\/strong><\/h2>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\">VWD je rijetka bolesti i nije svaki ljekar s njom upoznat. Zato bi <strong>kona\u010dnu dijagnozu trebao postaviti ljekar specijalista za poreme\u0107aje krvarenja<\/strong>. Dijagnoza VWD-a obavezno obuhvata cijeli proces. Va\u0161 ljekar za po\u010detak treba biti upoznat s bilo kakvim krvarenjem kod Vas i \u010dlanova Va\u0161e porodice. Ove informacije nazivaju se &#8220;historija krvarenja&#8221;. Kako bi ocijenio cjelokupnu historiju krvarenja, ljekar \u0107e vam postaviti niz pitanja. Ako historija krvarenja ukazuje na to da mo\u017eda imate poreme\u0107aj krvarenja, krv Vam mora biti analizirana u specijaliziranom laboratoriju.<sup>1<\/sup> Na temelju rezultata krvnih pretraga ljekar \u0107e postaviti kona\u010dnu dijagnozu.<\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<p class=\"full\"><strong>\u0160to prije dobijete dijagnozu, prije \u0107ete mo\u0107i po\u010deti donositi informisane odluke o svom lije\u010denju i na\u010dinu \u017eivota.<\/strong><\/p>\n<\/div>\n\n<div class=\"default-block container\">\n<h6>Literatura<\/h6>\n<\/div>\n\n<div class=\"default-block container\">\n<ol><div class=\"default-block container\">\n<li>Corrales-Medina FF et al. <em>Blood Rev <\/em>2022; 101018.<a id=\"_msocom_1\"><\/a><\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li><a id=\"_msocom_1\"><\/a>Leebeek FWG and Eikenboom JCJ. <em>N Engl J Med<\/em> 2016; 21:2067-80.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Srivastava A et al. <em>Haemophilia <\/em>2020; 26(Suppl 6):1-158.<\/li>\n<\/div>\n\n<div class=\"default-block container\">\n<li>Connell NT et al. <em>Blood Adv <\/em>2021; 5:301-25.<\/li>\n<\/div><\/ol>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>Von Willebrandova bolest (VWD) je naj\u010de\u0161\u0107i poreme\u0107aj krvarenja Kada je krvna \u017eila povrije\u0111ena, dio crvenih krvnih \u0107elija se sljepljuje kako bi zatvorile ranu i zaustavile krvarenje. Taj se proces naziva zgru\u0161avanje. Kod osoba s poreme\u0107ajima krvarenja, kao \u0161to su VWB ili hemofilija, zgru\u0161avanje krvi ne funkcioni\u0161e pravilno. Zato su osobe s VWD-om sklonije \u010de\u0161\u0107em i [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":231,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"inline_featured_image":false},"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v20.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Saznajte vi\u0161e o von Willebrandovoj bolesti - Bosnia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/vwdtest.com\/ba\/von-willebrand-disease\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Saznajte vi\u0161e o von Willebrandovoj bolesti - Bosnia\" \/>\n<meta property=\"og:description\" content=\"Von Willebrandova bolest (VWD) je naj\u010de\u0161\u0107i poreme\u0107aj krvarenja Kada je krvna \u017eila povrije\u0111ena, dio crvenih krvnih \u0107elija se sljepljuje kako bi zatvorile ranu i zaustavile krvarenje. Taj se proces naziva zgru\u0161avanje. Kod osoba s poreme\u0107ajima krvarenja, kao \u0161to su VWB ili hemofilija, zgru\u0161avanje krvi ne funkcioni\u0161e pravilno. Zato su osobe s VWD-om sklonije \u010de\u0161\u0107em i [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/vwdtest.com\/ba\/von-willebrand-disease\/\" \/>\n<meta property=\"og:site_name\" content=\"Bosnia\" \/>\n<meta property=\"article:modified_time\" content=\"2025-09-26T11:52:04+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/vwdtest.com\/ba\/wp-content\/uploads\/sites\/60\/2023\/02\/hero2.webp\" \/>\n\t<meta property=\"og:image:width\" content=\"774\" \/>\n\t<meta property=\"og:image:height\" content=\"927\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/webp\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data1\" content=\"4 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/vwdtest.com\/ba\/von-willebrand-disease\/\",\"url\":\"https:\/\/vwdtest.com\/ba\/von-willebrand-disease\/\",\"name\":\"Saznajte vi\u0161e o von Willebrandovoj bolesti - Bosnia\",\"isPartOf\":{\"@id\":\"https:\/\/vwdtest.com\/ba\/#website\"},\"datePublished\":\"2023-02-13T13:51:56+00:00\",\"dateModified\":\"2025-09-26T11:52:04+00:00\",\"breadcrumb\":{\"@id\":\"https:\/\/vwdtest.com\/ba\/von-willebrand-disease\/#breadcrumb\"},\"inLanguage\":\"en-US\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/vwdtest.com\/ba\/von-willebrand-disease\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/vwdtest.com\/ba\/von-willebrand-disease\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\/\/vwdtest.com\/ba\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Saznajte vi\u0161e o von Willebrandovoj bolesti\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/vwdtest.com\/ba\/#website\",\"url\":\"https:\/\/vwdtest.com\/ba\/\",\"name\":\"Bosnia\",\"description\":\"\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/vwdtest.com\/ba\/?s={search_term_string}\"},\"query-input\":\"required name=search_term_string\"}],\"inLanguage\":\"en-US\"}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Saznajte vi\u0161e o von Willebrandovoj bolesti - Bosnia","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/vwdtest.com\/ba\/von-willebrand-disease\/","og_locale":"en_US","og_type":"article","og_title":"Saznajte vi\u0161e o von Willebrandovoj bolesti - Bosnia","og_description":"Von Willebrandova bolest (VWD) je naj\u010de\u0161\u0107i poreme\u0107aj krvarenja Kada je krvna \u017eila povrije\u0111ena, dio crvenih krvnih \u0107elija se sljepljuje kako bi zatvorile ranu i zaustavile krvarenje. Taj se proces naziva zgru\u0161avanje. Kod osoba s poreme\u0107ajima krvarenja, kao \u0161to su VWB ili hemofilija, zgru\u0161avanje krvi ne funkcioni\u0161e pravilno. 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